Gene Information
Gene NameHSD17B10
OrganismHomo sapiens (Human)
Gene Length261
Protein Names3-hydroxyacyl-CoA dehydrogenase type-2 (EC 1.1.1.35) (17-beta-estradiol 17-dehydrogenase) (EC 1.1.1.62) (2-methyl-3-hydroxybutyryl-CoA dehydrogenase) (MHBD) (3-alpha-(17-beta)-hydroxysteroid dehydrogenase (NAD(+))) (EC 1.1.1.239) (3-hydroxy-2-methylbutyryl-CoA dehydrogenase) (EC 1.1.1.178) (3-hydroxyacyl-CoA dehydrogenase type II) (3alpha(or 20beta)-hydroxysteroid dehydrogenase) (EC 1.1.1.53) (7-alpha-hydroxysteroid dehydrogenase) (EC 1.1.1.159) (Endoplasmic reticulum-associated amyloid beta-peptide-binding protein) (Mitochondrial ribonuclease P protein 2) (Mitochondrial RNase P protein 2) (Short chain dehydrogenase/reductase family 5C member 1) (Short-chain type dehydrogenase/reductase XH98G2) (Type II HADH)
Target Name3-hydroxyacyl-coa dehydrogenase type-2
Target TypeNA
Gene Age1488 ( ENSG00000072506 )
Evolutionary StageEuk+Bac
AlphaFoldDBQ99714
Gene CardHSD17B10
Uniprot IDQ99714
PfamPF00106
In ASDno
Allosteric Predictionyes (0.269479246)
Ortholog in AnimalsAlpaca_ HSD17B10 ( ortholog_one2one )
Dog_ HSD17B10 ( ortholog_one2one )
GuineaPig_ HSD17B10 ( ortholog_one2one )
Macaque_ HSD17B10 ( ortholog_one2one )
Mouse_ Hsd17b10 ( ortholog_one2one )
Pig_ HSD17B10 ( ortholog_one2one )
Rat_ Hsd17b10 ( ortholog_one2one )
Rabbit_ HSD17B10 ( ortholog_one2one )
OhnologsNA
ParalogsSDR9C7, HSD17B14, HSD17B7, HSD11B2, DHRS12, RDH12, HSDL1, HSD17B4, DHRS9, RDH11, RDH16, HSD17B8, HSD17B11, BDH1, WWOX, HSD17B2, RDH5, DHRS3, HSD17B13, HSD17B12, SDR16C5, HSD17B1, RDH10, HSD17B3, HSD17B6
TissueNA
Tissue SpecificityUbiquitously expressed in normal tissues but is overexpressed in neurons affected in AD. {ECO:0000269|PubMed:9338779}.
Pharmacological Animal ModelsNULL(Chimpanzee);NULL(Mouse);NULL(Rat);0.022222(Rabbit)
Gene Ontology
(biological process)
Gene Ontology
(cellular component)
Gene Ontology
(molecular function)
PDB 1SO8  (X-ray  2.30A  1U7T  (X-ray  2.00A  2O23  (X-ray  1.20A  7ONU  (EM  3.00A 
DBSNP rs104886492  rs587777651  rs28935476  rs28935475  rs886041974  rs1556894502  rs122461163  rs62626305 
Subcellular location [CC]Mitochondrion {ECO:0000269|PubMed:12917011, ECO:0000269|PubMed:18984158}. Mitochondrion matrix, mitochondrion nucleoid {ECO:0000269|PubMed:24703694}.
Mouse PG classificationNA
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