Gene Information
Gene NameTMLHE
OrganismHomo sapiens (Human)
Gene Length421
Protein NamesTrimethyllysine dioxygenase, mitochondrial (EC 1.14.11.8) (Epsilon-trimethyllysine 2-oxoglutarate dioxygenase) (Epsilon-trimethyllysine hydroxylase) (TML hydroxylase) (TML-alpha-ketoglutarate dioxygenase) (TML dioxygenase) (TMLD)
Target Nametrimethyllysine dioxygenase, mitochondrial
Target TypeNA
Gene Age950 ( ENSG00000185973 )
Evolutionary StageOpisthokonta
AlphaFoldDBQ9NVH6
Gene CardTMLHE
Uniprot IDQ9NVH6
PfamPF06155; PF02668
In ASDno
Allosteric Predictionno (-0.934448496)
Ortholog in AnimalsAlpaca_ TMLHE ( ortholog_one2one )
GuineaPig_ TMLHE ( ortholog_one2one )
Macaque_ TMLHE ( ortholog_one2one )
Pig_ TMLHE ( ortholog_one2one )
Rat_ Tmlhe ( ortholog_one2one )
Rabbit_ TMLHE ( ortholog_one2one )
OhnologsNA
ParalogsBBOX1
TissueNA
Tissue SpecificityAll isoforms, but isoform 8, are widely expressed in adult and fetal tissues. Isoform 8 is restricted to heart and skeletal muscle. {ECO:0000269|PubMed:15754339, ECO:0000269|PubMed:17408883}.
Pharmacological Animal ModelsNA
Gene Ontology
(biological process)
Gene Ontology
(cellular component)
Gene Ontology
(molecular function)
PDB NA 
DBSNP rs869320708  rs782001959 
Subcellular location [CC]Mitochondrion matrix {ECO:0000269|PubMed:15754339}.
Mouse PG classificationNA
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