Gene Information
Gene NameSMCHD1
OrganismHomo sapiens (Human)
Gene Length2005
Protein NamesStructural maintenance of chromosomes flexible hinge domain-containing protein 1 (SMC hinge domain-containing protein 1) (EC 3.6.1.-)
Target NameNA
Target TypeNA
Gene Age1292 ( ENSG00000101596 )
Evolutionary StageEumetazoa
AlphaFoldDBA6NHR9
Gene CardSMCHD1
Uniprot IDA6NHR9
PfamPF06470
In ASDno
Allosteric Predictionno (-0.9998169)
Ortholog in AnimalsAlpaca_ SMCHD1 ( ortholog_one2one )
Dog_ SMCHD1 ( ortholog_one2one )
GuineaPig_ SMCHD1 ( ortholog_one2one )
Macaque_ SMCHD1 ( ortholog_one2one )
Mouse_ Smchd1 ( ortholog_one2one )
Pig_ SMCHD1 ( ortholog_one2one )
Rat_ Smchd1 ( ortholog_one2one )
Rabbit_ SMCHD1 ( ortholog_one2one )
OhnologsNA
ParalogsNA
TissueNA
Tissue SpecificityNA
Pharmacological Animal Models0.000730(Chimpanzee);NULL(Mouse);NULL(Rat);NULL(Rabbit)
Gene Ontology
(biological process)
Gene Ontology
(cellular component)
Gene Ontology
(molecular function)
PDB 6MW7  (X-ray  2.19A 
DBSNP rs1135402737  rs1135402738  rs1057519645  rs1057519646  rs1057519646  rs1057519643  rs1057519644  rs1135402739  rs1057519641  rs1135402740  rs1135402741  rs746679988  rs886041921  rs1057519639  rs1057519640  rs1057519642  rs1135402742  rs1135402743  rs1135402744  rs1135402745  rs397518422  rs886042392  rs397514623  rs2276092  rs633422  rs9961682 
Subcellular location [CC]Chromosome {ECO:0000269|PubMed:24790221, ECO:0000269|PubMed:25294876}. Note=Recruited to inactivated chromosome X in females by Xist RNA (By similarity). Localizes at sites of DNA damage at double-strand breaks (DSBs) (PubMed:25294876, PubMed:24790221). {ECO:0000250|UniProtKB:Q6P5D8, ECO:0000269|PubMed:24790221, ECO:0000269|PubMed:25294876}.
Mouse PG classificationLPG
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