Gene Information
Gene NameUCHL1
OrganismHomo sapiens (Human)
Gene Length223
Protein NamesUbiquitin carboxyl-terminal hydrolase isozyme L1 (UCH-L1) (EC 3.4.19.12) (Neuron cytoplasmic protein 9.5) (PGP 9.5) (PGP9.5) (Ubiquitin thioesterase L1)
Target Nameubiquitin carboxyl-terminal hydrolase isozyme l1
Target TypeNA
Gene Age544 ( ENSG00000154277 )
Evolutionary StageEukaryota
AlphaFoldDBP09936
Gene CardUCHL1
Uniprot IDP09936
PfamPF01088
In ASDno
Allosteric Predictionno (-0.230611811)
Ortholog in AnimalsAlpaca_ UCHL1 ( ortholog_one2one )
GuineaPig_ UCHL1 ( ortholog_one2one )
Macaque_ UCHL1 ( ortholog_one2one )
Mouse_ Uchl1 ( ortholog_one2one )
Pig_ UCHL1 ( ortholog_one2one )
Rat_ Uchl1 ( ortholog_one2one )
Rabbit_ UCHL1 ( ortholog_one2one )
OhnologsUCHL3
ParalogsBAP1, UCHL3, UCHL5
Tissuesubstantia.nigra
Tissue SpecificityFound in neuronal cell bodies and processes throughout the neocortex (at protein level). Expressed in neurons and cells of the diffuse neuroendocrine system and their tumors. Weakly expressed in ovary. Down-regulated in brains from Parkinson disease and Alzheimer disease patients. {ECO:0000269|PubMed:14722078, ECO:0000269|PubMed:9790970}.
Pharmacological Animal ModelsNA
Gene Ontology
(biological process)
Gene Ontology
(cellular component)
Gene Ontology
(molecular function)
PDB 2ETL  (X-ray  2.40A  2LEN  (NMR  3IFW  (X-ray  2.40A  3IRT  (X-ray  2.80A  3KVF  (X-ray  2.80A  3KW5  (X-ray  2.83A  4DM9  (X-ray  2.35A  4JKJ  (X-ray  2.15A 
DBSNP rs397515634  rs5030732  rs121917767  rs768996179  rs1057519600 
Subcellular location [CC]Cytoplasm {ECO:0000269|PubMed:19261853}. Endoplasmic reticulum membrane {ECO:0000269|PubMed:19261853};
Lipid-anchor {ECO:0000269|PubMed:19261853}. Note=About 30% of total UCHL1 is associated with membranes in brain.
Mouse PG classificationNA
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