Gene Information
Gene NameOGDH
OrganismHomo sapiens (Human)
Gene Length1023
Protein Names2-oxoglutarate dehydrogenase complex component E1 (E1o) (OGDC-E1) (OGDH-E1) (EC 1.2.4.2) (2-oxoglutarate dehydrogenase, mitochondrial) (Alpha-ketoglutarate dehydrogenase) (Alpha-KGDH-E1) (Thiamine diphosphate (ThDP)-dependent 2-oxoglutarate dehydrogenase)
Target Namealpha-ketoglutarate dehydrogenase
Target TypeClinical trial target
Gene Age1488 ( ENSG00000105953 )
Evolutionary StageEuk+Bac
AlphaFoldDBQ02218
Gene CardOGDH
Uniprot IDQ02218
PfamPF16078; PF00676; PF16870; PF02779
In ASDno
Allosteric Predictionyes (0.392750251)
Ortholog in AnimalsAlpaca_ OGDH ( ortholog_one2many )
Dog_ OGDH ( ortholog_one2one )
GuineaPig_ OGDH ( ortholog_one2one )
Macaque_ OGDH ( ortholog_one2one )
Mouse_ Ogdh ( ortholog_one2one )
Pig_ OGDH ( ortholog_one2one )
Rat_ Ogdh ( ortholog_one2one )
Rabbit_ OGDH ( ortholog_one2one )
OhnologsOGDHL
ParalogsOGDHL, DHTKD1
TissueNA
Tissue SpecificityNA
Pharmacological Animal ModelsNULL(Chimpanzee);NULL(Mouse);NULL(Rat);0.031579(Rabbit)
Gene Ontology
(biological process)
Gene Ontology
(cellular component)
Gene Ontology
(molecular function)
PDB 3ERY  (X-ray  1.95A  7WGR  (EM  2.92A 
DBSNP rs2070607 
Subcellular location [CC]Mitochondrion {ECO:0000269|PubMed:29211711}. Nucleus {ECO:0000269|PubMed:29211711}. Note=Mainly localizes in the mitochondrion. A small fraction localizes to the nucleus, where the 2-oxoglutarate dehydrogenase complex is required for histone succinylation. {ECO:0000269|PubMed:29211711}.
Mouse PG classificationLPG
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