Gene Information
Gene NameNDUFS4
OrganismHomo sapiens (Human)
Gene Length175
Protein NamesNADH dehydrogenase [ubiquinone] iron-sulfur protein 4, mitochondrial (Complex I-18 kDa) (CI-18 kDa) (Complex I-AQDQ) (CI-AQDQ) (NADH-ubiquinone oxidoreductase 18 kDa subunit)
Target Namenadh dehydrogenase [ubiquinone] iron-sulfur protein 4, mitochondrial
Target TypeNA
Gene Age1488 ( ENSG00000164258 )
Evolutionary StageEuk+Bac
AlphaFoldDBO43181
Gene CardNDUFS4
Uniprot IDO43181
PfamPF04800
In ASDno
Allosteric Predictionno (-0.512096844)
Ortholog in AnimalsAlpaca_ NDUFS4 ( ortholog_one2one )
Macaque_ NDUFS4 ( ortholog_one2one )
Mouse_ Ndufs4 ( ortholog_one2one )
Pig_ NDUFS4 ( ortholog_one2one )
Rat_ Ndufs4 ( ortholog_one2one )
Rabbit_ NDUFS4 ( ortholog_one2one )
OhnologsNA
ParalogsWDR93
TissueNA
Tissue SpecificityNA
Pharmacological Animal Models0.359685(Chimpanzee);0.329993(Mouse);NULL(Rat);0.262308(Rabbit)
Gene Ontology
(biological process)
Gene Ontology
(cellular component)
Gene Ontology
(molecular function)
PDB 5XTB  (EM  3.40A  5XTD  (EM  3.70A  5XTH  (EM  3.90A  5XTI  (EM  17.40A 
DBSNP rs747359752  rs1044692 
Subcellular location [CC]Mitochondrion inner membrane {ECO:0000269|PubMed:11181577, ECO:0000269|PubMed:12611891, ECO:0000269|PubMed:31206022};
Peripheral membrane protein {ECO:0000269|PubMed:12611891};
Matrix side {ECO:0000269|PubMed:12611891}. Note=The interaction with BCAP31 mediates mitochondria localization. {ECO:0000269|PubMed:31206022}.
Mouse PG classificationHPG
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