Gene Information
Gene NameCHSY1
OrganismHomo sapiens (Human)
Gene Length802
Protein NamesChondroitin sulfate synthase 1 (EC 2.4.1.175) (EC 2.4.1.226) (Chondroitin glucuronyltransferase 1) (Chondroitin synthase 1) (ChSy-1) (Glucuronosyl-N-acetylgalactosaminyl-proteoglycan 4-beta-N-acetylgalactosaminyltransferase 1) (N-acetylgalactosaminyl-proteoglycan 3-beta-glucuronosyltransferase 1) (N-acetylgalactosaminyltransferase 1)
Target NameNA
Target TypeNA
Gene Age886 ( ENSG00000131873 )
Evolutionary StageEumetazoa
AlphaFoldDBQ86X52
Gene CardCHSY1
Uniprot IDQ86X52
PfamPF05679
In ASDno
Allosteric Predictionno (-1.35628582)
Ortholog in AnimalsDog_ CHSY1 ( ortholog_one2one )
GuineaPig_ CHSY1 ( ortholog_one2one )
Macaque_ CHSY1 ( ortholog_one2one )
Mouse_ Chsy1 ( ortholog_one2one )
Pig_ CHSY1 ( ortholog_one2one )
Rat_ Chsy1 ( ortholog_one2one )
Rabbit_ CHSY1 ( ortholog_one2one )
OhnologsNA
ParalogsCHSY3, CHPF, CHPF2, B4GALNT3, B4GALNT4, CSGALNACT2, CSGALNACT1
TissueNA
Tissue SpecificityUbiquitous, with the highest levels in placenta. Detected at low levels in brain, heart, skeletal muscle, colon, thymus, spleen, kidney, liver, adrenal gland, mammary gland, stomach, small intestine, lung and peripheral blood leukocytes. {ECO:0000269|PubMed:11514575, ECO:0000269|PubMed:12907687}.
Pharmacological Animal ModelsNA
Gene Ontology
(biological process)
Gene Ontology
(cellular component)
Gene Ontology
(molecular function)
PDB NA 
DBSNP rs3743193  rs387906985  rs4426333 
Subcellular location [CC]Golgi apparatus, Golgi stack membrane {ECO:0000305|PubMed:11514575};
Single-pass type II membrane protein {ECO:0000305|PubMed:11514575}. Secreted {ECO:0000269|PubMed:21129727}.
Mouse PG classificationHPG
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