Gene Information
Gene NameCHSY3
OrganismHomo sapiens (Human)
Gene Length882
Protein NamesChondroitin sulfate synthase 3 (EC 2.4.1.175) (EC 2.4.1.226) (Carbohydrate synthase 2) (Chondroitin glucuronyltransferase 3) (Chondroitin synthase 2) (ChSy-2) (Glucuronosyl-N-acetylgalactosaminyl-proteoglycan 4-beta-N-acetylgalactosaminyltransferase II) (N-acetylgalactosaminyl-proteoglycan 3-beta-glucuronosyltransferase 3) (N-acetylgalactosaminyltransferase 3)
Target NameNA
Target TypeNA
Gene Age645 ( ENSG00000198108 )
Evolutionary StageMammalia
AlphaFoldDBQ70JA7
Gene CardCHSY3
Uniprot IDQ70JA7
PfamPF05679
In ASDno
Allosteric Predictionno (-1.09208763)
Ortholog in AnimalsAlpaca_ CHSY3 ( ortholog_one2one )
Dog_ CHSY3 ( ortholog_one2one )
Macaque_ CHSY3 ( ortholog_one2one )
Mouse_ Chsy3 ( ortholog_one2one )
Pig_ CHSY3 ( ortholog_one2one )
Rat_ Chsy3 ( ortholog_one2one )
Rabbit_ CHSY3 ( ortholog_one2one )
OhnologsNA
ParalogsCHSY1, CHPF, CHPF2, B4GALNT3, B4GALNT4, CSGALNACT2, CSGALNACT1
TissueNA
Tissue SpecificityDetected at low levels in brain, cerebral cortex, uterus and small intestine. {ECO:0000269|PubMed:12907687}.
Pharmacological Animal ModelsNA
Gene Ontology
(biological process)
Gene Ontology
(cellular component)
Gene Ontology
(molecular function)
PDB NA 
DBSNP rs10068403  rs2015018 
Subcellular location [CC]Golgi apparatus, Golgi stack membrane {ECO:0000305|PubMed:12907687};
Single-pass type II membrane protein {ECO:0000305|PubMed:12907687}.
Mouse PG classificationNA
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