Gene Information
Gene NameBRCA1
OrganismHomo sapiens (Human)
Gene Length1863
Protein NamesBreast cancer type 1 susceptibility protein (EC 2.3.2.27) (RING finger protein 53) (RING-type E3 ubiquitin transferase BRCA1)
Target NameNA
Target TypeNA
Gene Age18 ( ENSG00000012048 )
Evolutionary StageEumetazoa
AlphaFoldDBP38398
Gene CardBRCA1
Uniprot IDP38398
PfamPF00533; PF12820; PF00097
In ASDno
Allosteric Predictionyes (0.602716258)
Ortholog in AnimalsAlpaca_ BRCA1 ( ortholog_one2one )
Dog_ BRCA1 ( ortholog_one2one )
Macaque_ BRCA1 ( ortholog_one2one )
Mouse_ Brca1 ( ortholog_one2one )
Pig_ BRCA1 ( ortholog_one2one )
Rat_ Brca1 ( ortholog_one2one )
Rabbit_ BRCA1 ( ortholog_one2one )
OhnologsNA
ParalogsNA
TissueNA
Tissue SpecificityIsoform 1 and isoform 3 are widely expressed. Isoform 3 is reduced or absent in several breast and ovarian cancer cell lines.
Pharmacological Animal ModelsNULL(Chimpanzee);NULL(Mouse);0.150722(Rat);0.056159(Rabbit)
Gene Ontology
(biological process)
Gene Ontology
(cellular component)
Gene Ontology
(molecular function)
PDB 1JM7  (NMR  1JNX  (X-ray  2.50A  1N5O  (X-ray  2.80A  1OQA  (NMR  1T15  (X-ray  1.85A  1T29  (X-ray  2.30A  1T2U  (X-ray  2.80A  1T2V  (X-ray  3.30A  1Y98  (X-ray  2.50A  2ING  (X-ray  3.60A  3COJ  (X-ray  3.21A  3K0H  (X-ray  2.70A  3K0K  (X-ray  2.70A  3K15  (X-ray  2.80A  3K16  (X-ray  3.00A  3PXA  (X-ray  2.55A  3PXB  (X-ray  2.50A  3PXC  (X-ray  2.80A  3PXD  (X-ray  2.80A  3PXE  (X-ray  2.85A  4IFI  (X-ray  2.20A  4IGK  (X-ray  1.75A  4JLU  (X-ray  3.50A  4OFB  (X-ray  3.05A  4U4A  (X-ray  3.51A  4Y18  (X-ray  3.50A  4Y2G  (X-ray  2.50A  6G2I  (EM  5.90A  7JZV  (EM  3.90A  7LYB  (EM  3.28A 
DBSNP rs786203152  rs80357017  rs80356929  rs80357406  rs80357438  rs769650474  rs28897672  rs80357064  rs55851803  rs80357102  rs80356913  rs28897673  rs80357413  rs55971303  rs748876625  rs28897674  rs80357325  rs55688530  rs80357090  rs80357001  rs80357396  rs80356865  rs28897675  rs80357244  rs80357244  rs8176153  rs80357015  rs1799950  rs80358325  rs56128296  rs56046357  rs397508869  rs80357224  rs397508893  rs80357250  rs4986850  rs28897681  rs4986845  rs80357114  rs80357467  rs876660005  rs28897682  rs56082113  rs28897683  rs751656678  rs80357337  rs1800709  rs80356892  rs41286300  rs799917  rs80357480  rs397508994  rs4986847  rs397509022  rs4986848  rs1800704  rs397509034  rs16941  rs4986852  rs397509037  rs80357184  rs41293447  rs80357228  rs2227945  rs80357272  rs16942  rs56214134  rs1060502347  rs80356923  rs80356876  rs28897687  rs28897686  rs587782190  rs80357217  rs1450793674  rs273900719  rs80357407  rs28897689  rs28897690  rs80357306  rs1800707  rs80357492  rs273900729  rs41293455  rs4986849  rs80357486  rs397507232  rs80357389  rs1800744  rs55815649  rs56158747  rs80356943  rs1799966  rs8176219  rs80356862  rs4986854  rs80357465  rs80357048  rs1800726  rs80356938  rs879254042  rs1799967  rs80357390  rs28897695  rs80357169  rs80356890  rs80357043  rs397509218  rs730882166  rs80358344  rs80357061  rs397507239  rs80357034  rs80187739  rs80356993  rs41293459  rs55770810  rs80356860  rs80356860  rs28897696  rs80357094  rs80357239  rs56195342  rs397509238  rs45553935  rs80356937  rs80357227  rs80357227  rs786202389  rs80357462  rs397509246  rs80357281  rs80357463  rs1597804426  rs863224765  rs41293463  rs41293463  rs1800757  rs80357474  rs398122697  rs80357069  rs80357078  rs397509275  rs80356920  rs1800751  rs80356959  rs80357183 
Subcellular location [CC]Nucleus {ECO:0000269|PubMed:15133502, ECO:0000269|PubMed:17525340, ECO:0000269|PubMed:20160719, ECO:0000269|PubMed:21144835, ECO:0000269|PubMed:26778126, ECO:0000269|PubMed:9528852}. Chromosome {ECO:0000269|PubMed:23269703, ECO:0000269|PubMed:25472942, ECO:0000269|PubMed:26778126}. Cytoplasm {ECO:0000269|PubMed:20160719}. Note=Localizes at sites of DNA damage at double-strand breaks (DSBs);
recruitment to DNA damage sites is mediated by ABRAXAS1 and the BRCA1-A complex (PubMed:26778126). Translocated to the cytoplasm during UV-induced apoptosis (PubMed:20160719). {ECO:0000269|PubMed:20160719, ECO:0000269|PubMed:26778126}.;
[Isoform 3]: Cytoplasm.;
[Isoform 5]: Cytoplasm {ECO:0000269|PubMed:8972225}.
Mouse PG classificationLPG
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