Gene Information
Gene NameCHCHD4
OrganismHomo sapiens (Human)
Gene Length142
Protein NamesMitochondrial intermembrane space import and assembly protein 40 (Coiled-coil-helix-coiled-coil-helix domain-containing protein 4)
Target NameNA
Target TypeNA
Gene Age987 ( ENSG00000163528 )
Evolutionary StageEukaryota
AlphaFoldDBQ8N4Q1
Gene CardCHCHD4
Uniprot IDQ8N4Q1
PfamPF06747
In ASDno
Allosteric Predictionno (-1.122680668)
Ortholog in AnimalsAlpaca_ CHCHD4 ( ortholog_one2one )
Dog_ CHCHD4 ( ortholog_one2one )
GuineaPig_ CHCHD4 ( ortholog_one2one )
Mouse_ AU015836 ( ortholog_one2many )
Mouse_ Chchd4 ( ortholog_one2many )
Pig_ CHCHD4 ( ortholog_one2many )
Rat_ AABR07067813.1 ( ortholog_one2many )
Rat_ Chchd4 ( ortholog_one2many )
Rabbit_ CHCHD4 ( ortholog_one2one )
OhnologsNA
ParalogsNA
TissueNA
Tissue SpecificityExpressed in all tissues tested, suggesting an ubiquitous expression. {ECO:0000269|PubMed:16185709}.
Pharmacological Animal ModelsNULL(Chimpanzee);NULL(Mouse);NULL(Rat);0.088889(Rabbit)
Gene Ontology
(biological process)
Gene Ontology
(cellular component)
Gene Ontology
(molecular function)
PDB 2K3J  (NMR  2L0Y  (NMR 
DBSNP NA 
Subcellular location [CC]Mitochondrion intermembrane space {ECO:0000269|PubMed:16185709, ECO:0000269|PubMed:23186364, ECO:0000269|PubMed:23676665, ECO:0000269|PubMed:26004228}.
Mouse PG classificationNA
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