Gene Information
Gene NamePAPPA
OrganismHomo sapiens (Human)
Gene Length1627
Protein NamesPappalysin-1 (EC 3.4.24.79) (Insulin-like growth factor-dependent IGF-binding protein 4 protease) (IGF-dependent IGFBP-4 protease) (IGFBP-4ase) (Pregnancy-associated plasma protein A) (PAPP-A)
Target Namepappalysin-1
Target TypeNA
Gene Age645 ( ENSG00000182752 )
Evolutionary StageEumetazoa
AlphaFoldDBQ13219
Gene CardPAPPA
Uniprot IDQ13219
PfamPF05572; PF00084
In ASDno
Allosteric Predictionno (-0.063191896)
Ortholog in AnimalsAlpaca_ PAPPA ( ortholog_one2one )
Dog_ PAPPA ( ortholog_one2one )
GuineaPig_ PAPPA ( ortholog_one2one )
Macaque_ PAPPA ( ortholog_one2one )
Mouse_ Pappa ( ortholog_one2one )
Pig_ PAPPA ( ortholog_one2one )
Rat_ Pappa1 ( ortholog_one2one )
Rabbit_ PAPPA ( ortholog_one2one )
OhnologsPAPPA2
ParalogsCR1L, SUSD3, F13B, SELP, SEZ6L2, CFHR2, CFHR1, CSMD1, APOH, SELE, SRPX, SVEP1, SEZ6, C8A, CD55, CSMD2, PAPPA2, SUSD6, C4BPA, C9, CR1, SELL, CFB, CD46, C4BPB, CR2, C7, CSMD3, CFHR3, CFH, SEZ6L, CFHR4, CFHR5, SRPX2, C8B, PRF1, SUSD4, C6, C2
Tissueplacenta
Tissue SpecificityHigh levels in placenta and pregnancy serum. In placenta, expressed in X cells in septa and anchoring villi, and in syncytiotrophoblasts in the chorionic villi. Lower levels are found in a variety of other tissues including kidney, myometrium, endometrium, ovaries, breast, prostate, bone marrow, colon, fibroblasts and osteoblasts. {ECO:0000269|PubMed:10077652, ECO:0000269|PubMed:10491647, ECO:0000269|PubMed:7508748, ECO:0000269|PubMed:7526035}.
Pharmacological Animal ModelsNULL(Chimpanzee);0.001000(Mouse);NULL(Rat);NULL(Rabbit)
Gene Ontology
(biological process)
Gene Ontology
(cellular component)
Gene Ontology
(molecular function)
PDB NA 
DBSNP rs417012  rs445159  rs117124330  rs7020782 
Subcellular location [CC]Secreted {ECO:0000269|PubMed:10077652}.
Mouse PG classificationNA
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