Gene Information
Gene NameATXN7
OrganismHomo sapiens (Human)
Gene Length892
Protein NamesAtaxin-7 (Spinocerebellar ataxia type 7 protein)
Target NameNA
Target TypeNA
Gene Age950 ( ENSG00000163635 )
Evolutionary StageEumetazoa
AlphaFoldDBO15265
Gene CardATXN7
Uniprot IDO15265
PfamPF08313
In ASDno
Allosteric Predictionyes (0.082042815)
Ortholog in AnimalsAlpaca_ ATXN7 ( ortholog_one2one )
Dog_ ATXN7 ( ortholog_one2one )
GuineaPig_ ATXN7 ( ortholog_one2one )
Macaque_ ATXN7 ( ortholog_one2one )
Mouse_ Atxn7 ( ortholog_one2one )
Pig_ ATXN7 ( ortholog_one2one )
Rat_ Atxn7 ( ortholog_one2one )
Rabbit_ ATXN7 ( ortholog_one2one )
OhnologsATXN7L1, ATXN7L2
ParalogsATXN7L1, ATXN7L3, ATXN7L3B, ATXN7L2
TissueNA
Tissue Specificity[Isoform a]: Isoform a is expressed in CNS, but is expressed predominantly in the peripherical tissues. {ECO:0000269|PubMed:12533095}.;
[Isoform b]: Isoform b is expressed in CNS (PubMed:12533095). Also highly expressed in the frontal lobe, skeletal muscle and spinal cord and is expressed at a lower level in the lung, lymphoblast and intestine (PubMed:12533095). {ECO:0000269|PubMed:12533095}.
Pharmacological Animal ModelsNA
Gene Ontology
(biological process)
Gene Ontology
(cellular component)
Gene Ontology
(molecular function)
PDB 2KKR  (NMR  7KTR  (EM  2.93A  7KTS  (EM  19.09A 
DBSNP rs1053338  rs3733124  rs1053340  rs3774729 
Subcellular location [CC][Isoform a]: Nucleus {ECO:0000269|PubMed:12533095, ECO:0000269|PubMed:16314424, ECO:0000269|PubMed:22100762}. Nucleus, nucleolus {ECO:0000269|PubMed:10441328}. Nucleus matrix {ECO:0000269|PubMed:10441328}. Cytoplasm, cytoskeleton {ECO:0000269|PubMed:22100762}. Note=In addition to a diffuse distribution throughout the nucleus, it is associated with the nuclear matrix and the nucleolus (PubMed:10441328). It is able to shuttle between the nucleus and cytoplasm (PubMed:16314424). {ECO:0000269|PubMed:10441328, ECO:0000269|PubMed:16314424}.;
[Isoform b]: Cytoplasm {ECO:0000269|PubMed:12533095}.
Mouse PG classificationHPG
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