Gene Information
Gene NameMTHFD2L
OrganismHomo sapiens (Human)
Gene Length347
Protein NamesBifunctional methylenetetrahydrofolate dehydrogenase/cyclohydrolase 2, mitochondrial (NADP-dependent methylenetetrahydrofolate dehydrogenase 2-like protein) (MTHFD2-like) [Includes: NAD-dependent methylenetetrahydrofolate dehydrogenase (EC 1.5.1.15) (EC 1.5.1.5); Methenyltetrahydrofolate cyclohydrolase (EC 3.5.4.9)]
Target NameNA
Target TypeNA
Gene Age>4290 ( ENSG00000163738 )
Evolutionary StageCellular_organisms
AlphaFoldDBQ9H903
Gene CardMTHFD2L
Uniprot IDQ9H903
PfamPF00763; PF02882
In ASDno
Allosteric Predictionno (-0.543254902)
Ortholog in AnimalsAlpaca_ MTHFD2L ( ortholog_one2one )
Dog_ MTHFD2L ( ortholog_one2one )
Macaque_ MTHFD2L ( ortholog_one2one )
Mouse_ Mthfd2l ( ortholog_one2one )
Pig_ MTHFD2L ( ortholog_one2one )
Rat_ Mthfd2l ( ortholog_one2one )
Rabbit_ MTHFD2L ( ortholog_one2one )
OhnologsMTHFD2
ParalogsMTHFD1L, MTHFD1, MTHFD2
TissueNA
Tissue SpecificityIsoform 1, isoform 4 and isoform 5 are expressed in brain and placenta. {ECO:0000269|PubMed:21163947}.
Pharmacological Animal ModelsNA
Gene Ontology
(biological process)
Gene Ontology
(cellular component)
Gene Ontology
(molecular function)
PDB NA 
DBSNP NA 
Subcellular location [CC]Mitochondrion inner membrane {ECO:0000250|UniProtKB:D3ZUA0};
Peripheral membrane protein {ECO:0000250|UniProtKB:D3ZUA0};
Matrix side {ECO:0000250|UniProtKB:D3ZUA0}.
Mouse PG classificationNA
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