Gene Information
Gene NamePITX2
OrganismHomo sapiens (Human)
Gene Length317
Protein NamesPituitary homeobox 2 (ALL1-responsive protein ARP1) (Homeobox protein PITX2) (Paired-like homeodomain transcription factor 2) (RIEG bicoid-related homeobox transcription factor) (Solurshin)
Target NameNA
Target TypeNA
Gene Age132 ( ENSG00000164093 )
Evolutionary StageEumetazoa
AlphaFoldDBQ99697
Gene CardPITX2
Uniprot IDQ99697
PfamPF00046; PF03826
In ASDno
Allosteric Predictionno (-0.309280774)
Ortholog in AnimalsAlpaca_ PITX2 ( ortholog_one2one )
Dog_ PITX2 ( ortholog_one2one )
Macaque_ PITX2 ( ortholog_one2one )
Pig_ PITX2 ( ortholog_one2one )
Rabbit_ PITX2 ( ortholog_one2one )
OhnologsPITX1, PITX3
ParalogsARGFX, PAX7, PAX3, ALX4, PAX2, UNCX, RAX2, PAX8, DMBX1, DPRX, PAX5, ISX, ALX3, RHOXF2B, RHOXF2, GSC2, SEBOX, RAX, DRGX, ARX, RHOXF1, PITX3, PRRX1, SHOX, SHOX2, PRRX2, OTX2, PAX4, EVX1, PAX1, PHOX2A, CRX, PHOX2B, EVX2, ALX1, VSX2, MIXL1, DUXA, PAX6, OTP, HESX1, NOBOX, PROP1, PAX9, GSC, ESX1, DUXB, DUX4, PITX1, OTX1
Tissueplacenta
Tissue SpecificityNA
Pharmacological Animal ModelsNA
Gene Ontology
(biological process)
Gene Ontology
(cellular component)
Gene Ontology
(molecular function)
PDB 2L7F  (NMR  2L7M  (NMR  2LKX  (NMR 
DBSNP rs104893857  rs104893862  rs1057519484  rs104893858  rs104893861  rs121909249  rs121909248  rs387906810  rs104893859 
Subcellular location [CC]Nucleus.
Mouse PG classificationHPG
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