Gene Information
Gene NamePCSK6
OrganismHomo sapiens (Human)
Gene Length969
Protein NamesProprotein convertase subtilisin/kexin type 6 (EC 3.4.21.-) (Paired basic amino acid cleaving enzyme 4) (Subtilisin-like proprotein convertase 4) (SPC4) (Subtilisin/kexin-like protease PACE4)
Target NameNA
Target TypeNA
Gene Age1488 ( ENSG00000140479 )
Evolutionary StageEuk+Bac
AlphaFoldDBP29122
Gene CardPCSK6
Uniprot IDP29122
PfamPF14843; PF01483; PF00082; PF08686; PF16470
In ASDno
Allosteric Predictionno (-0.464888649)
Ortholog in AnimalsAlpaca_ PCSK6 ( ortholog_one2one )
Dog_ PCSK6 ( ortholog_one2one )
GuineaPig_ PCSK6 ( ortholog_one2one )
Macaque_ PCSK6 ( ortholog_one2one )
Mouse_ Pcsk6 ( ortholog_one2one )
Pig_ PCSK6 ( ortholog_one2one )
Rat_ Pcsk6 ( ortholog_one2one )
Rabbit_ PCSK6 ( ortholog_one2one )
OhnologsPCSK4, PCSK1
ParalogsPCSK1, TPP2, MBTPS1, PCSK7, PCSK5, PCSK9, PCSK4, FURIN, PCSK2
Tissueliver, spleen
Tissue SpecificityEach PACE4 isoform exhibits a unique restricted distribution. Isoform PACE4A-I is expressed in heart, brain, placenta, lung, skeletal muscle, kidney, pancreas, but at comparatively higher levels in the liver. Isoform PACE4A-II is at least expressed in placenta. Isoform PACE4B was only found in the embryonic kidney cell line from which it was isolated. Isoform PACE4C and isoform PACE4D are expressed in placenta. Isoform PACE4E-I is expressed in cerebellum, placenta and pituitary. Isoform PACE4E-II is at least present in cerebellum.
Pharmacological Animal ModelsNA
Gene Ontology
(biological process)
Gene Ontology
(cellular component)
Gene Ontology
(molecular function)
PDB NA 
DBSNP rs1058260 
Subcellular location [CC][Isoform PACE4A-I]: Secreted.;
[Isoform PACE4A-II]: Secreted.;
[Isoform PACE4C]: Endoplasmic reticulum. Note=Not secreted, remains probably in zymogen form in endoplasmic reticulum.;
[Isoform PACE4CS]: Endoplasmic reticulum. Note=Not secreted, remains probably in zymogen form in endoplasmic reticulum.;
[Isoform PACE4E-I]: Endomembrane system;
Peripheral membrane protein. Note=Retained intracellularly probably through a hydrophobic cluster in their C-terminus.;
[Isoform PACE4E-II]: Endomembrane system;
Peripheral membrane protein. Note=Retained intracellularly probably through a hydrophobic cluster in their C-terminus.;
[Isoform PACE4B]: Secreted.
Mouse PG classificationNA
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