Gene Information
Gene NameTMEM126A
OrganismHomo sapiens (Human)
Gene Length195
Protein NamesTransmembrane protein 126A
Target NameNA
Target TypeNA
Gene Age680 ( ENSG00000171202 )
Evolutionary StageEumetazoa
AlphaFoldDBQ9H061
Gene CardTMEM126A
Uniprot IDQ9H061
PfamPF07114
In ASDno
Allosteric Predictionno (-1.46682977)
Ortholog in AnimalsAlpaca_ TMEM126A ( ortholog_one2one )
Dog_ TMEM126A ( ortholog_one2one )
GuineaPig_ TMEM126A ( ortholog_one2one )
Macaque_ TMEM126A ( ortholog_one2one )
Mouse_ Tmem126a ( ortholog_one2one )
Pig_ TMEM126A ( ortholog_one2one )
Rat_ Tmem126a ( ortholog_one2one )
OhnologsNA
ParalogsTMEM126B
TissueNA
Tissue SpecificityStrongly expressed in brain, cerebellum, skeletal muscle, testis. High expression also found in fetal brain, fetal retinal pigmentary epithelium, and fetal retina. Highly expressed in retinal ganglion cells. {ECO:0000269|PubMed:19327736, ECO:0000269|PubMed:23500070}.
Pharmacological Animal ModelsNA
Gene Ontology
(biological process)
Gene Ontology
(cellular component)
Gene Ontology
(molecular function)
PDB NA 
DBSNP rs11556797 
Subcellular location [CC]Mitochondrion inner membrane {ECO:0000269|PubMed:19327736, ECO:0000269|PubMed:23500070};
Multi-pass membrane protein {ECO:0000269|PubMed:19327736, ECO:0000269|PubMed:23500070}.
Mouse PG classificationNA
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