Gene Information
Gene NameEXOSC9
OrganismHomo sapiens (Human)
Gene Length439
Protein NamesExosome complex component RRP45 (Autoantigen PM/Scl 1) (Exosome component 9) (P75 polymyositis-scleroderma overlap syndrome-associated autoantigen) (Polymyositis/scleroderma autoantigen 1) (Polymyositis/scleroderma autoantigen 75 kDa) (PM/Scl-75)
Target NameNA
Target TypeNA
Gene Age645 ( ENSG00000123737 )
Evolutionary StageEukaryota
AlphaFoldDBQ06265
Gene CardEXOSC9
Uniprot IDQ06265
PfamPF01138; PF03725
In ASDno
Allosteric Predictionno (-0.942664626)
Ortholog in AnimalsAlpaca_ EXOSC9 ( ortholog_one2one )
Dog_ EXOSC9 ( ortholog_one2one )
GuineaPig_ EXOSC9 ( ortholog_one2one )
Macaque_ EXOSC9 ( ortholog_one2one )
Mouse_ Exosc9 ( ortholog_one2one )
Pig_ EXOSC9 ( ortholog_one2one )
Rat_ Exosc9 ( ortholog_one2one )
Rabbit_ EXOSC9 ( ortholog_one2one )
OhnologsNA
ParalogsEXOSC8, EXOSC7
TissueNA
Tissue SpecificityNA
Pharmacological Animal ModelsNULL(Chimpanzee);NULL(Mouse);0.074168(Rat);0.089027(Rabbit)
Gene Ontology
(biological process)
Gene Ontology
(cellular component)
Gene Ontology
(molecular function)
PDB 2NN6  (X-ray  3.35A  6D6Q  (EM  3.45A  6D6R  (EM  3.45A  6H25  (EM  3.80A 
DBSNP rs139632595  rs1803183  rs1051881 
Subcellular location [CC]Cytoplasm {ECO:0000269|PubMed:11782436}. Nucleus {ECO:0000269|PubMed:24105744}. Nucleus, nucleolus {ECO:0000269|PubMed:24105744}. Nucleus, nucleoplasm {ECO:0000269|PubMed:24105744}. Note=Colocalizes with SETX in nuclear foci upon induction of transcription-related DNA damage at the S phase (PubMed:24105744). {ECO:0000269|PubMed:24105744}.;
[Isoform 1]: Nucleus, nucleolus.;
[Isoform 2]: Nucleus, nucleolus.;
[Isoform 3]: Nucleus. Note=Excluded from the nucleolus.
Mouse PG classificationNA
click here to return to the previous page