Gene Information
Gene NameNPC2
OrganismHomo sapiens (Human)
Gene Length151
Protein NamesNPC intracellular cholesterol transporter 2 (Epididymal secretory protein E1) (Human epididymis-specific protein 1) (He1) (Niemann-Pick disease type C2 protein)
Target NameNA
Target TypeNA
Gene Age1488 ( ENSG00000119655 )
Evolutionary StageEumetazoa
AlphaFoldDBP61916
Gene CardNPC2
Uniprot IDP61916
PfamPF02221
In ASDno
Allosteric Predictionno (-0.372527379)
Ortholog in AnimalsAlpaca_ NPC2 ( ortholog_one2one )
Dog_ NPC2 ( ortholog_one2many )
GuineaPig_ NPC2 ( ortholog_one2one )
Macaque_ NPC2 ( ortholog_one2one )
Mouse_ Npc2 ( ortholog_one2one )
Pig_ NPC2 ( ortholog_one2one )
Rat_ Npc2 ( ortholog_one2one )
Rabbit_ NPC2 ( ortholog_one2one )
OhnologsNA
ParalogsNA
TissueNA
Tissue SpecificityDetected in gallbladder bile (PubMed:21315718). Detected in fibroblasts, kidney, liver, spleen, small intestine, placenta and testis (at protein level) (PubMed:11125141). Epididymis. {ECO:0000269|PubMed:11125141, ECO:0000269|PubMed:19664597, ECO:0000269|PubMed:21315718}.
Pharmacological Animal Models0.000730(Chimpanzee);0.001000(Mouse);NULL(Rat);NULL(Rabbit)
Gene Ontology
(biological process)
Gene Ontology
(cellular component)
Gene Ontology
(molecular function)
PDB 5KWY  (X-ray  2.40A  6W5V  (EM  4.00A 
DBSNP rs151220873  rs80358261  rs1555345993  rs11694  rs4688  rs143960270  rs80358264  rs104894458 
Subcellular location [CC]Secreted {ECO:0000269|PubMed:11125141, ECO:0000269|PubMed:15937921, ECO:0000269|PubMed:19723497, ECO:0000269|PubMed:21315718}. Endoplasmic reticulum {ECO:0000269|PubMed:19723497}. Lysosome {ECO:0000269|PubMed:15937921, ECO:0000269|PubMed:19723497, ECO:0000305|PubMed:11125141}. Note=Interaction with cell-surface M6PR mediates endocytosis and targeting to lysosomes. {ECO:0000305|PubMed:11125141}.
Mouse PG classificationNA
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