Gene Information
Gene NameMYBPHL
OrganismHomo sapiens (Human)
Gene Length354
Protein NamesMyosin-binding protein H-like
Target NameNA
Target TypeNA
Gene Age244 ( ENSG00000221986 )
Evolutionary StageEumetazoa
AlphaFoldDBA2RUH7
Gene CardMYBPHL
Uniprot IDA2RUH7
PfamPF00041; PF07679
In ASDno
Allosteric Predictionno (-1.76288941)
Ortholog in AnimalsAlpaca_ MYBPHL ( ortholog_one2one )
Dog_ MYBPHL ( ortholog_one2one )
GuineaPig_ MYBPHL ( ortholog_one2one )
Macaque_ MYBPHL ( ortholog_one2one )
Mouse_ Mybphl ( ortholog_one2one )
Pig_ MYBPHL ( ortholog_one2one )
Rat_ Mybphl ( ortholog_one2one )
Rabbit_ MYBPHL ( ortholog_one2one )
OhnologsNA
ParalogsMYOM1, MYBPC1, MYBPC2, MYOM3, MYBPH, MYOM2, FNDC3A, MYBPC3, OBSL1, IGSF22, FNDC3B
Tissueheart, left.atrium, mitral.valve, atrium
Tissue SpecificityExpressed in heart, with higher expression in the atria. {ECO:0000269|PubMed:28778945, ECO:0000269|PubMed:31292467}.;
[Isoform 1]: Expressed in left atrium and ventricle, arteria mammaria interna and skeletal muscle. {ECO:0000269|PubMed:31292467}.;
[Isoform 2]: Expressed specifically en the left atrium. {ECO:0000269|PubMed:31292467}.
Pharmacological Animal ModelsNA
Gene Ontology
(biological process)
Gene Ontology
(cellular component)
Gene Ontology
(molecular function)
PDB NA 
DBSNP rs629001 
Subcellular location [CC]Cytoplasm, myofibril, sarcomere {ECO:0000305|PubMed:28778945}.
Mouse PG classificationNA
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