Gene Information
Gene NameMMACHC
OrganismHomo sapiens (Human)
Gene Length282
Protein NamesCyanocobalamin reductase / alkylcobalamin dealkylase (Alkylcobalamin:glutathione S-alkyltransferase) (EC 2.5.1.151) (CblC) (Cyanocobalamin reductase (cyanide-eliminating)) (EC 1.16.1.6) (Methylmalonic aciduria and homocystinuria type C protein) (MMACHC)
Target Namemethylmalonic aciduria and homocystinuria type c protein
Target TypeNA
Gene Age1488 ( ENSG00000132763 )
Evolutionary StageEumetazoa
AlphaFoldDBQ9Y4U1
Gene CardMMACHC
Uniprot IDQ9Y4U1
PfamPF16690
In ASDno
Allosteric Predictionno (-0.904843476)
Ortholog in AnimalsAlpaca_ MMACHC ( ortholog_one2one )
GuineaPig_ MMACHC ( ortholog_one2one )
Macaque_ MMACHC ( ortholog_one2one )
Mouse_ Mmachc ( ortholog_one2one )
Pig_ MMACHC ( ortholog_one2one )
Rat_ Mmachc ( ortholog_one2one )
Rabbit_ MMACHC ( ortholog_one2one )
OhnologsNA
ParalogsNA
TissueNA
Tissue SpecificityWidely expressed. Expressed at higher level in fetal liver. Also expressed in spleen, lymph node, thymus and bone marrow. Weakly or not expressed in peripheral blood leukocytes. {ECO:0000269|PubMed:16311595}.
Pharmacological Animal ModelsNA
Gene Ontology
(biological process)
Gene Ontology
(cellular component)
Gene Ontology
(molecular function)
PDB 3SBY  (X-ray  2.71A  3SBZ  (X-ray  2.00A  3SC0  (X-ray  1.95A  3SOM  (X-ray  2.40A  5UOS  (X-ray  2.51A 
DBSNP rs546099787  rs121918240  rs372670428  rs140522266  rs140522266  rs1553162910  rs1002571805  rs370596113  rs121918243  rs200895671  rs1233135084  rs371753672  rs538023671  rs35219601 
Subcellular location [CC]Cytoplasm, cytosol {ECO:0000269|PubMed:23270877}.
Mouse PG classificationLPG
click here to return to the previous page