Gene Information
Gene NameALDH4A1
OrganismHomo sapiens (Human)
Gene Length563
Protein NamesDelta-1-pyrroline-5-carboxylate dehydrogenase, mitochondrial (P5C dehydrogenase) (EC 1.2.1.88) (Aldehyde dehydrogenase family 4 member A1) (L-glutamate gamma-semialdehyde dehydrogenase)
Target Namedelta-1-pyrroline-5-carboxylate dehydrogenase, mitochondrial
Target TypeNA
Gene Age1714 ( ENSG00000159423 )
Evolutionary StageEuk+Bac
AlphaFoldDBP30038
Gene CardALDH4A1
Uniprot IDP30038
PfamPF00171
In ASDno
Allosteric Predictionyes (0.333360997)
Ortholog in AnimalsAlpaca_ ALDH4A1 ( ortholog_one2one )
Dog_ ALDH4A1 ( ortholog_one2one )
GuineaPig_ ALDH4A1 ( ortholog_one2one )
Macaque_ ALDH4A1 ( ortholog_one2one )
Mouse_ Aldh4a1 ( ortholog_one2one )
Pig_ ALDH4A1 ( ortholog_one2one )
Rabbit_ ALDH4A1 ( ortholog_one2one )
OhnologsNA
ParalogsALDH7A1, ALDH1B1, ALDH3A2, ALDH1A1, ALDH3B1, ALDH3B2, ALDH3A1, ALDH2, ALDH9A1, ALDH1A2, ALDH6A1, ALDH5A1, ALDH1L1, ALDH1A3, ALDH1L2, ALDH8A1, ALDH16A1
Tissuekidney
Tissue SpecificityHighest expression is found in liver followed by skeletal muscle, kidney, heart, brain, placenta, lung and pancreas.
Pharmacological Animal ModelsNA
Gene Ontology
(biological process)
Gene Ontology
(cellular component)
Gene Ontology
(molecular function)
PDB 3V9G  (X-ray  2.50A  3V9H  (X-ray  2.40A  3V9I  (X-ray  2.85A  4OE5  (X-ray  1.95A 
DBSNP rs146450609  rs137852937  rs2230709  rs6695033 
Subcellular location [CC]Mitochondrion matrix.
Mouse PG classificationNA
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