Gene Information
Gene NameACTN2
OrganismHomo sapiens (Human)
Gene Length894
Protein NamesAlpha-actinin-2 (Alpha-actinin skeletal muscle isoform 2) (F-actin cross-linking protein)
Target NameNA
Target TypeNA
Gene Age1292 ( ENSG00000077522 )
Evolutionary StageEukaryota
AlphaFoldDBP35609
Gene CardACTN2
Uniprot IDP35609
PfamPF00307; PF08726; PF00435
In ASDno
Allosteric Predictionyes (1.096927364)
Ortholog in AnimalsAlpaca_ ACTN2 ( ortholog_one2one )
Dog_ ACTN2 ( ortholog_one2one )
GuineaPig_ ACTN2 ( ortholog_one2one )
Macaque_ ACTN2 ( ortholog_one2one )
Mouse_ Actn2 ( ortholog_one2one )
Pig_ ACTN2 ( ortholog_one2one )
Rat_ Actn2 ( ortholog_one2one )
Rabbit_ ACTN2 ( ortholog_one2one )
OhnologsACTN1, ACTN4
ParalogsACTN3, DSP, SPTBN5, ACTN4, MICAL2, DMD, SYNE3, GAS2L2, SPTBN2, FLNB, SPTAN1, SYNE2, PLEC, EPPK1, SYNE1, CLMN, DYTN, MICAL3, PKHD1, SMTNL2, DRP2, UTRN, PKHD1L1, MICAL1, SPTBN1, MACF1, ACTN1, DST, SPTB, GAS2L3, FLNC, FLNA, DTNA, SPTA1, DTNB, SPTBN4
Tissueheart, skeletal.muscle, left.ventricle
Tissue SpecificityExpressed in both skeletal and cardiac muscle.
Pharmacological Animal ModelsNA
Gene Ontology
(biological process)
Gene Ontology
(cellular component)
Gene Ontology
(molecular function)
PDB 1H8B  (NMR  1HCI  (X-ray  2.80A  1QUU  (X-ray  2.50A  4D1E  (X-ray  3.50A  5A36  (X-ray  2.00A  5A37  (X-ray  1.88A  5A38  (X-ray  1.90A  5A4B  (X-ray  2.01A  6SWT  (X-ray  1.20A  6TS3  (X-ray  1.28A  7A8T  (X-ray  2.69A  7A8U  (X-ray  3.80A  7B55  (X-ray  1.60A  7B56  (X-ray  1.45A  7B57  (X-ray  1.95A 
DBSNP rs121434525  rs727502886  rs1572114611  rs786205144  rs1572140109  rs200248944  rs200631005  rs35997569  rs786204951  rs1572148902 
Subcellular location [CC]Cytoplasm, myofibril, sarcomere, Z line {ECO:0000269|PubMed:11171996, ECO:0000269|PubMed:19932097, ECO:0000269|PubMed:30701273}. Note=Colocalizes with MYOZ1 and FLNC at the Z-lines of skeletal muscle.
Mouse PG classificationNA
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