Gene Information
Gene NameLRRC8A
OrganismHomo sapiens (Human)
Gene Length810
Protein NamesVolume-regulated anion channel subunit LRRC8A (Leucine-rich repeat-containing protein 8A) (HsLRRC8A) (Swelling protein 1)
Target NameNA
Target TypeNA
Gene Age645 ( ENSG00000136802 )
Evolutionary StageEukaryota
AlphaFoldDBQ8IWT6
Gene CardLRRC8A
Uniprot IDQ8IWT6
PfamPF13855; PF12534
In ASDno
Allosteric Predictionno (-0.670329139)
Ortholog in AnimalsAlpaca_ LRRC8A ( ortholog_one2one )
Dog_ LRRC8A ( ortholog_one2one )
GuineaPig_ LRRC8A ( ortholog_one2one )
Macaque_ LRRC8A ( ortholog_one2one )
Mouse_ Lrrc8a ( ortholog_one2one )
Pig_ LRRC8A ( ortholog_one2one )
Rat_ Lrrc8a ( ortholog_one2one )
Rabbit_ LRRC8A ( ortholog_one2one )
OhnologsLRRC8E, LRRC8C, LRRC8D
ParalogsLRRC8B, LRRIQ4, LRRC18, LRCH4, LRRK1, LRRC58, LRRD1, PHLPP1, ERBIN, LRRC8C, LRCH2, MFHAS1, SCRIB, LRRC1, LRRC2, PIDD1, LRRC30, LRRC27, LRRC8E, LRRC7, LRCH1, LRRC10, LRRC10B, LRRC40, SHOC2, PHLPP2, LRCH3, LRRC69, LRRC39, LRRC28, LRRC8D
TissueNA
Tissue SpecificityExpressed in brain, kidney, ovary, lung, liver, heart, and fetal brain and liver. Found at high levels in bone marrow;
lower levels are detected in peripheral blood cells. Expressed on T-cells as well as on B-lineage cells. {ECO:0000269|PubMed:10718198, ECO:0000269|PubMed:14660746}.
Pharmacological Animal ModelsNULL(Chimpanzee);NULL(Mouse);NULL(Rat);0.066667(Rabbit)
Gene Ontology
(biological process)
Gene Ontology
(cellular component)
Gene Ontology
(molecular function)
PDB 5ZSU  (EM  4.25A  6DJB  (EM  4.40A 
DBSNP rs769167142 
Subcellular location [CC]Cell membrane {ECO:0000269|PubMed:24725410, ECO:0000269|PubMed:24782309, ECO:0000269|PubMed:24790029, ECO:0000269|PubMed:26824658, ECO:0000305|PubMed:29769723};
Multi-pass membrane protein {ECO:0000269|PubMed:24725410, ECO:0000269|PubMed:24782309, ECO:0000269|PubMed:24790029, ECO:0000269|PubMed:30095067, ECO:0000269|PubMed:30127360}. Lysosome membrane {ECO:0000269|PubMed:33139539};
Multi-pass membrane protein {ECO:0000269|PubMed:24725410, ECO:0000269|PubMed:24782309, ECO:0000269|PubMed:24790029, ECO:0000269|PubMed:30095067, ECO:0000269|PubMed:30127360}. Note=Mainly localizes to the cell membrane, with some intracellular localization to lysosomes. {ECO:0000269|PubMed:33139539}.
Mouse PG classificationNA
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