Gene Information
Gene NameACAD8
OrganismHomo sapiens (Human)
Gene Length415
Protein NamesIsobutyryl-CoA dehydrogenase, mitochondrial (IBDH) (EC 1.3.8.-) (Activator-recruited cofactor 42 kDa component) (ARC42) (Acyl-CoA dehydrogenase family member 8) (ACAD-8)
Target Nameisobutyryl-coa dehydrogenase, mitochondrial
Target TypeNA
Gene Age1064 ( ENSG00000151498 )
Evolutionary StageEuk+Bac
AlphaFoldDBQ9UKU7
Gene CardACAD8
Uniprot IDQ9UKU7
PfamPF00441; PF02770; PF02771
In ASDno
Allosteric Predictionno (-0.349604039)
Ortholog in AnimalsAlpaca_ ACAD8 ( ortholog_one2one )
Dog_ ACAD8 ( ortholog_one2one )
GuineaPig_ ACAD8 ( ortholog_one2one )
Macaque_ ACAD8 ( ortholog_one2one )
Mouse_ Acad8 ( ortholog_one2one )
Pig_ ACAD8 ( ortholog_one2one )
Rat_ Acad8 ( ortholog_one2one )
OhnologsNA
ParalogsACOX1, ACAD11, ACADM, ACAD9, IVD, GCDH, ACOXL, ACAD10, ACADS, ACOX3, ACOX2, ACADVL, ACADSB, ACADL
TissueNA
Tissue SpecificityDetected at comparable levels in all tissues examined (heart, lung, brain, skeletal muscle, pancreas and placenta). Weakly expressed in liver and kidney.
Pharmacological Animal ModelsNA
Gene Ontology
(biological process)
Gene Ontology
(cellular component)
Gene Ontology
(molecular function)
PDB 1RX0  (X-ray  1.77A 
DBSNP rs374317179  rs367857040  rs371449613  rs121908418  rs759877257  rs121908422  rs200620279  rs778823613  rs367996531 
Subcellular location [CC]Mitochondrion {ECO:0000269|PubMed:11013134, ECO:0000269|PubMed:12359132}.
Mouse PG classificationLPG
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