Gene Information
Gene NameLBR
OrganismHomo sapiens (Human)
Gene Length615
Protein NamesDelta(14)-sterol reductase LBR (Delta-14-SR) (EC 1.3.1.70) (3-beta-hydroxysterol Delta (14)-reductase) (C-14 sterol reductase) (C14SR) (Integral nuclear envelope inner membrane protein) (LMN2R) (Lamin-B receptor) (Sterol C14-reductase)
Target NameNA
Target TypeNA
Gene Age1714 ( ENSG00000143815 )
Evolutionary StageEukaryota
AlphaFoldDBQ14739
Gene CardLBR
Uniprot IDQ14739
PfamPF01222; PF09465
In ASDno
Allosteric Predictionyes (0.282406749)
Ortholog in AnimalsAlpaca_ LBR ( ortholog_one2one )
Dog_ LBR ( ortholog_one2one )
Macaque_ LBR ( ortholog_one2one )
Mouse_ Lbr ( ortholog_one2one )
Pig_ LBR ( ortholog_one2one )
Rat_ AABR07021955.1 ( ortholog_one2one )
Rabbit_ LBR ( ortholog_one2one )
OhnologsTM7SF2, DHCR7
ParalogsTM7SF2, DHCR7
TissueNA
Tissue SpecificityExpressed in the bone marrow, liver, heart, adrenal gland, lung, placenta and uterus (PubMed:16784888). Expressed in osteoclasts and osteoblast-like cells (PubMed:21327084). {ECO:0000269|PubMed:16784888, ECO:0000269|PubMed:21327084}.
Pharmacological Animal ModelsNULL(Chimpanzee);NULL(Mouse);NULL(Rat);0.06386(Rabbit)
Gene Ontology
(biological process)
Gene Ontology
(cellular component)
Gene Ontology
(molecular function)
PDB 2DIG  (NMR 
DBSNP rs869312905  rs137852605  rs2230419  rs2230420  rs2275601  rs200180113  rs587777171  rs374343844  rs137852606  rs587777172  rs573510559 
Subcellular location [CC]Nucleus inner membrane {ECO:0000269|PubMed:8157662};
Multi-pass membrane protein {ECO:0000255}. Endoplasmic reticulum membrane {ECO:0000269|PubMed:21327084}. Cytoplasm {ECO:0000269|PubMed:21327084}. Nucleus {ECO:0000269|PubMed:21327084}. Note=Nucleus;
nuclear rim. {ECO:0000269|PubMed:21327084}.
Mouse PG classificationNA
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