Gene Information
Gene NameUSB1
OrganismHomo sapiens (Human)
Gene Length265
Protein NamesU6 snRNA phosphodiesterase 1 (hUsb1) (3'-5' RNA exonuclease USB1) (EC 4.6.1.-) (Mutated in poikiloderma with neutropenia protein 1) (Mutated in PN protein 1) (hMpn1)
Target NameNA
Target TypeNA
Gene Age1488 ( ENSG00000103005 )
Evolutionary StageEukaryota
AlphaFoldDBQ9BQ65
Gene CardUSB1
Uniprot IDQ9BQ65
PfamPF09749
In ASDno
Allosteric Predictionno (-1.681769017)
Ortholog in AnimalsAlpaca_ USB1 ( ortholog_one2one )
Dog_ USB1 ( ortholog_one2one )
GuineaPig_ USB1 ( ortholog_one2one )
Macaque_ USB1 ( ortholog_one2one )
Mouse_ Usb1 ( ortholog_one2one )
Pig_ USB1 ( ortholog_one2one )
Rat_ Usb1 ( ortholog_one2one )
OhnologsNA
ParalogsNA
TissueNA
Tissue SpecificityNA
Pharmacological Animal ModelsNULL(Chimpanzee);NULL(Mouse);0.001823(Rat);NULL(Rabbit)
Gene Ontology
(biological process)
Gene Ontology
(cellular component)
Gene Ontology
(molecular function)
PDB 4H7W  (X-ray  1.10A  5V1M  (X-ray  1.47A  6D2Z  (X-ray  1.18A  6D30  (X-ray  1.17A  6D31  (X-ray  1.20A 
DBSNP rs35025252  rs16959641 
Subcellular location [CC]Nucleus {ECO:0000255|HAMAP-Rule:MF_03040, ECO:0000269|PubMed:22899009, ECO:0000269|PubMed:23022480}.
Mouse PG classificationNA
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