Gene Information
Gene NameACSM1
OrganismHomo sapiens (Human)
Gene Length577
Protein NamesAcyl-coenzyme A synthetase ACSM1, mitochondrial (EC 6.2.1.2) (Acyl-CoA synthetase medium-chain family member 1) (Benzoate--CoA ligase) (EC 6.2.1.25) (Butyrate--CoA ligase 1) (Butyryl-coenzyme A synthetase 1) (Lipoate-activating enzyme) (Middle-chain acyl-CoA synthetase 1) (Xenobiotic/medium-chain fatty acid-CoA ligase HXM-B)
Target NameNA
Target TypeNA
Gene Age1488 ( ENSG00000166743 )
Evolutionary StageCellular_organisms
AlphaFoldDBQ08AH1
Gene CardACSM1
Uniprot IDQ08AH1
PfamPF00501; PF13193
In ASDno
Allosteric Predictionno (-0.709175995)
Ortholog in AnimalsAlpaca_ ACSM1 ( ortholog_one2one )
GuineaPig_ ACSM1 ( ortholog_one2one )
Macaque_ ACSM1 ( ortholog_one2one )
Mouse_ Acsm1 ( ortholog_one2one )
Rat_ Acsm1 ( ortholog_one2one )
Rabbit_ ACSM1 ( ortholog_one2one )
OhnologsACSM4
ParalogsACSM4, ACSS2, ACSM2B, ACSM2A, AACS, ACSM3, AASDH, ACSS3, ACSM5, ACSM6, ACSF2, ACSF3, ACSS1
TissueNA
Tissue SpecificityNA
Pharmacological Animal ModelsNA
Gene Ontology
(biological process)
Gene Ontology
(cellular component)
Gene Ontology
(molecular function)
PDB NA 
DBSNP rs16970511  rs8056709  rs16970453 
Subcellular location [CC]Mitochondrion matrix {ECO:0000250|UniProtKB:Q91VA0}. Mitochondrion {ECO:0000250|UniProtKB:Q91VA0}.
Mouse PG classificationNA
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