Gene Information
Gene NamePKD1
OrganismHomo sapiens (Human)
Gene Length4303
Protein NamesPolycystin-1 (PC1) (Autosomal dominant polycystic kidney disease 1 protein)
Target NameNA
Target TypeNA
Gene Age1064 ( ENSG00000008710 )
Evolutionary StageEumetazoa
AlphaFoldDBNA
Gene CardPKD1
Uniprot IDP98161
PfamPF00059; PF13855; PF00801; PF08016; PF01477; PF20519; PF02010; PF01822
In ASDno
Allosteric Predictionyes (0.456264521)
Ortholog in AnimalsGuineaPig_ PKD1 ( ortholog_one2one )
Macaque_ PKD1 ( ortholog_one2one )
Mouse_ Pkd1 ( ortholog_one2one )
Pig_ PKD1 ( ortholog_one2one )
Rat_ Pkd1 ( ortholog_one2one )
OhnologsNA
ParalogsPKDREJ, PKD1L2, PKD2L2, DENND5B, DENND5A, PKD2L1, LOXHD1, PKD1L3, PKD1L1, PKD2
TissueNA
Tissue SpecificityNA
Pharmacological Animal ModelsNULL(Chimpanzee);NULL(Mouse);0.002240(Rat);0.025(Rabbit)
Gene Ontology
(biological process)
Gene Ontology
(cellular component)
Gene Ontology
(molecular function)
PDB 1B4R  (NMR  6A70  (EM  3.60A 
DBSNP rs560049593  rs886038369  rs958271752  rs1567219544  rs199476099  rs1232180956  rs1555458892  rs58598099  rs149022148  rs1555458413  rs1616940  rs40433  rs199476100  rs2369063  rs1266492292  rs2549677  rs241573  rs573566419  rs146887330  rs1033550407  rs143690392  rs116092985  rs148164067  rs241572  rs761106434  rs139520275  rs241571  rs151176070  rs778028644  rs144137200  rs754890213  rs137978188  rs752388015  rs1383930225  rs140869992  rs139971481  rs200433577  rs1567187445  rs538769374  rs1555453210  rs1555453207  rs151257298  rs1161298621  rs2432404  rs3874655  rs200037070  rs28369051  rs758896945  rs748240352  rs2432405  rs778565182  rs9936785  rs374500158  rs1490043027  rs144557371  rs201238819  rs147350387  rs150568356  rs141717814  rs1800569  rs1800568  rs1596527405  rs144979397  rs1456510041  rs1057518897  rs151089809  rs367746233  rs534112936  rs149151043  rs1567177684  rs755522953  rs752447240  rs147788838  rs750780241  rs13337123  rs150189496  rs373952574  rs1555450487  rs1063401  rs117896488  rs17135779  rs200522524  rs778055216  rs9925969  rs1358566538  rs139945204  rs140791671  rs201780393  rs1242837732  rs781263445  rs371283948  rs776463508  rs140189010  rs45478794  rs141946034  rs34197769  rs79000340  rs781492044  rs1416373452  rs1555446576  rs1327414405  rs1167476946  rs142768096  rs10960  rs3209986  rs1306483854  rs1309138642  rs148478410  rs1282668884  rs115538130  rs547854563  rs114251396 
Subcellular location [CC]Cell membrane {ECO:0000269|PubMed:10339594, ECO:0000269|PubMed:20980620, ECO:0000269|PubMed:27214281, ECO:0000269|PubMed:27259053, ECO:0000269|PubMed:30093605};
Multi-pass membrane protein {ECO:0000269|PubMed:20980620, ECO:0000269|PubMed:30093605}. Cell projection, cilium {ECO:0000250|UniProtKB:O08852}. Endoplasmic reticulum {ECO:0000250|UniProtKB:O08852}. Golgi apparatus {ECO:0000250|UniProtKB:O08852}. Note=PKD1 localization to the plasma and ciliary membranes requires PKD2, is independent of PKD2 channel activity, and involves stimulation of PKD1 autoproteolytic cleavage at the GPS domain. PKD1:PKD2 interaction is required to reach the Golgi apparatus from endoplasmic reticulum and then traffic to the cilia (By similarity). Ciliary localization of PKD1 requires BBS1 and ARL6/BBS3 (By similarity). Cell surface localization requires GANAB (PubMed:27259053). {ECO:0000250|UniProtKB:O08852, ECO:0000269|PubMed:27259053}.
Mouse PG classificationHPG
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