Gene Information
Gene NameAGA
OrganismHomo sapiens (Human)
Gene Length346
Protein NamesN(4)-(beta-N-acetylglucosaminyl)-L-asparaginase (EC 3.5.1.26) (Aspartylglucosaminidase) (Glycosylasparaginase) (N4-(N-acetyl-beta-glucosaminyl)-L-asparagine amidase) [Cleaved into: Glycosylasparaginase alpha chain; Glycosylasparaginase beta chain]
Target NameNA
Target TypeNA
Gene Age987 ( ENSG00000038002 )
Evolutionary StageEukaryota
AlphaFoldDBP20933
Gene CardAGA
Uniprot IDP20933
PfamPF01112
In ASDno
Allosteric Predictionyes (0.325354056)
Ortholog in AnimalsAlpaca_ AGA ( ortholog_one2one )
Dog_ AGA ( ortholog_one2one )
GuineaPig_ AGA ( ortholog_one2one )
Macaque_ AGA ( ortholog_one2one )
Mouse_ Aga ( ortholog_one2one )
Pig_ AGA ( ortholog_one2one )
Rat_ Aga ( ortholog_one2one )
Rabbit_ AGA ( ortholog_one2one )
OhnologsNA
ParalogsASRGL1, TASP1
TissueNA
Tissue SpecificityNA
Pharmacological Animal ModelsNA
Gene Ontology
(biological process)
Gene Ontology
(cellular component)
Gene Ontology
(molecular function)
PDB 1APY  (X-ray  2.00A  1APZ  (X-ray  2.30A 
DBSNP rs74626221  rs121964907  rs121964909  rs386833421  rs121964908  rs386833427  rs2228119  rs192195150  rs121964904  rs386833433  rs386833432  rs386833434  rs121964905  rs121964906  rs56849061 
Subcellular location [CC]Lysosome.
Mouse PG classificationLPG
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