Gene Information
Gene NameLMBRD1
OrganismHomo sapiens (Human)
Gene Length540
Protein NamesLysosomal cobalamin transport escort protein LMBD1 (LMBD1) (HDAg-L-interacting protein NESI) (LMBR1 domain-containing protein 1) (Nuclear export signal-interacting protein)
Target NameNA
Target TypeNA
Gene Age645 ( ENSG00000168216 )
Evolutionary StageEukaryota
AlphaFoldDBQ9NUN5
Gene CardLMBRD1
Uniprot IDQ9NUN5
PfamPF04791
In ASDno
Allosteric Predictionno (-0.136369779)
Ortholog in AnimalsAlpaca_ LMBRD1 ( ortholog_one2one )
Dog_ LMBRD1 ( ortholog_one2one )
GuineaPig_ LMBRD1 ( ortholog_one2one )
Macaque_ LMBRD1 ( ortholog_one2one )
Mouse_ Lmbrd1 ( ortholog_one2one )
Pig_ LMBRD1 ( ortholog_one2one )
Rat_ Lmbrd1 ( ortholog_one2one )
Rabbit_ LMBRD1 ( ortholog_one2one )
OhnologsNA
ParalogsNA
TissueNA
Tissue SpecificityIsoform 3 is expressed in liver. {ECO:0000269|PubMed:15956556}.
Pharmacological Animal ModelsNA
Gene Ontology
(biological process)
Gene Ontology
(cellular component)
Gene Ontology
(molecular function)
PDB NA 
DBSNP rs12214456  rs17854411  rs12648 
Subcellular location [CC]Endoplasmic reticulum membrane {ECO:0000269|PubMed:27456980}. Lysosome membrane {ECO:0000269|PubMed:19136951, ECO:0000269|PubMed:27456980, ECO:0000269|PubMed:28572511, ECO:0000269|PubMed:33845046};
Multi-pass membrane protein {ECO:0000255}. Cell membrane {ECO:0000250|UniProtKB:Q8K0B2};
Multi-pass membrane protein {ECO:0000255}. Cytoplasmic vesicle, clathrin-coated vesicle {ECO:0000250|UniProtKB:Q8K0B2}.
Mouse PG classificationLPG
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