Gene Information
Gene NameP4HA1
OrganismHomo sapiens (Human)
Gene Length534
Protein NamesProlyl 4-hydroxylase subunit alpha-1 (4-PH alpha-1) (EC 1.14.11.2) (Procollagen-proline,2-oxoglutarate-4-dioxygenase subunit alpha-1)
Target Nameprolyl 4-hydroxylase subunit alpha-1
Target TypeNA
Gene Age645 ( ENSG00000122884 )
Evolutionary StageEukaryota
AlphaFoldDBP13674
Gene CardP4HA1
Uniprot IDP13674
PfamPF13640; PF08336
In ASDno
Allosteric Predictionyes (0.842013247)
Ortholog in AnimalsAlpaca_ P4HA1 ( ortholog_one2one )
Dog_ P4HA1 ( ortholog_one2one )
GuineaPig_ P4HA1 ( ortholog_one2one )
Macaque_ P4HA1 ( ortholog_one2one )
Mouse_ P4ha1 ( ortholog_one2one )
Pig_ P4HA1 ( ortholog_one2one )
Rat_ P4ha1 ( ortholog_one2one )
Rabbit_ P4HA1 ( ortholog_one2one )
OhnologsP4HA2
ParalogsP4HA2, P4HA3, P4HTM
TissueNA
Tissue SpecificityExpressed in the heart, liver, skeletal muscle, kidney, placenta, lung and pancreas. {ECO:0000269|PubMed:9211872}.
Pharmacological Animal ModelsNA
Gene Ontology
(biological process)
Gene Ontology
(cellular component)
Gene Ontology
(molecular function)
PDB 1TJC  (X-ray  2.30A  2V5F  (X-ray  2.03A  2YQ8  (X-ray  2.99A  4BT8  (X-ray  2.20A  4BT9  (X-ray  1.90A  4BTA  (X-ray  2.95A  4BTB  (X-ray  1.90A 
DBSNP NA 
Subcellular location [CC]Endoplasmic reticulum lumen.
Mouse PG classificationNA
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