Gene Information
Gene NameRPUSD4
OrganismHomo sapiens (Human)
Gene Length377
Protein NamesPseudouridylate synthase RPUSD4, mitochondrial (EC 5.4.99.-) (RNA pseudouridylate synthase domain-containing protein 4)
Target NameNA
Target TypeNA
Gene Age645 ( ENSG00000165526 )
Evolutionary StageEuk+Bac
AlphaFoldDBQ96CM3
Gene CardRPUSD4
Uniprot IDQ96CM3
PfamPF00849
In ASDno
Allosteric Predictionno (-2.102904432)
Ortholog in AnimalsAlpaca_ RPUSD4 ( ortholog_one2one )
Dog_ RPUSD4 ( ortholog_one2one )
GuineaPig_ RPUSD4 ( ortholog_one2one )
Macaque_ RPUSD4 ( ortholog_one2one )
Mouse_ Rpusd4 ( ortholog_one2one )
Pig_ RPUSD4 ( ortholog_one2one )
Rat_ Rpusd4 ( ortholog_one2one )
Rabbit_ RPUSD4 ( ortholog_one2one )
OhnologsNA
ParalogsRPUSD1, RPUSD2, RPUSD3
TissueNA
Tissue SpecificityNA
Pharmacological Animal ModelsNA
Gene Ontology
(biological process)
Gene Ontology
(cellular component)
Gene Ontology
(molecular function)
PDB 5UBA  (X-ray  1.54A 
DBSNP rs2282580  rs35468281  rs34809853  rs35157957 
Subcellular location [CC]Mitochondrion matrix {ECO:0000269|PubMed:23435261, ECO:0000269|PubMed:27974379, ECO:0000269|PubMed:28082677}. Nucleus {ECO:0000269|PubMed:23435261}. Cytoplasm {ECO:0000269|PubMed:23435261}. Note=Mainly localizes to mitochondrion (PubMed:23435261, PubMed:27974379, PubMed:28082677). Localizes to mitochondrial RNA granules, platforms for post-transcriptional RNA modification and ribosome assembly (PubMed:27974379, PubMed:28082677). Also found in nucleus and cytoplasm (PubMed:23435261). {ECO:0000269|PubMed:23435261, ECO:0000269|PubMed:27974379, ECO:0000269|PubMed:28082677}.
Mouse PG classificationNA
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