Gene Information
Gene NameITCH
OrganismHomo sapiens (Human)
Gene Length903
Protein NamesE3 ubiquitin-protein ligase Itchy homolog (Itch) (EC 2.3.2.26) (Atrophin-1-interacting protein 4) (AIP4) (HECT-type E3 ubiquitin transferase Itchy homolog) (NFE2-associated polypeptide 1) (NAPP1)
Target NameNA
Target TypeNA
Gene Age544 ( ENSG00000078747 )
Evolutionary StageEukaryota
AlphaFoldDBQ96J02
Gene CardITCH
Uniprot IDQ96J02
PfamPF00168; PF00632; PF00397
In ASDno
Allosteric Predictionno (-0.028250039)
Ortholog in AnimalsAlpaca_ ITCH ( ortholog_one2one )
Dog_ ITCH ( ortholog_one2one )
GuineaPig_ ITCH ( ortholog_one2one )
Macaque_ ITCH ( ortholog_one2one )
Mouse_ Itch ( ortholog_one2one )
Pig_ ITCH ( ortholog_one2one )
Rat_ Itch ( ortholog_one2one )
Rabbit_ ITCH ( ortholog_one2one )
OhnologsWWP1, WWP2
ParalogsHERC4, NEDD4, HECTD1, NEDD4L, UBE3B, HUWE1, SMURF1, AREL1, UBR5, HERC2, HECW2, HERC3, WWP1, UBE3A, UBE3C, SMURF2, HACE1, HECTD2, HECTD4, HECW1, WWP2, TRIP12, HERC5, HERC6
TissueNA
Tissue SpecificityWidely expressed.
Pharmacological Animal ModelsNA
Gene Ontology
(biological process)
Gene Ontology
(cellular component)
Gene Ontology
(molecular function)
PDB 2DMV  (NMR  2KYK  (NMR  2NQ3  (X-ray  1.80A  2P4R  (X-ray  2.00A  2YSF  (NMR  3TUG  (X-ray  2.27A  4ROF  (X-ray  2.03A  5C7M  (X-ray  3.03A  5CQ2  (X-ray  1.40A  5DWS  (X-ray  1.65A  5DZD  (X-ray  1.57A  5SXP  (X-ray  1.65A 
DBSNP NA 
Subcellular location [CC]Cell membrane {ECO:0000269|PubMed:14602072};
Peripheral membrane protein {ECO:0000305|PubMed:14602072};
Cytoplasmic side {ECO:0000305|PubMed:14602072}. Cytoplasm {ECO:0000269|PubMed:14602072}. Nucleus {ECO:0000269|PubMed:20858735}. Early endosome membrane {ECO:0000269|PubMed:14602072, ECO:0000269|PubMed:23146885, ECO:0000269|PubMed:24790097};
Peripheral membrane protein {ECO:0000305|PubMed:14602072, ECO:0000305|PubMed:23146885, ECO:0000305|PubMed:24790097};
Cytoplasmic side {ECO:0000305|PubMed:14602072, ECO:0000305|PubMed:23146885, ECO:0000305|PubMed:24790097}. Endosome membrane {ECO:0000269|PubMed:23146885};
Peripheral membrane protein {ECO:0000305|PubMed:23146885};
Cytoplasmic side {ECO:0000305|PubMed:23146885}. Note=May be recruited to exosomes by NDFIP1 (PubMed:18819914). Localizes to plasma membrane upon CXCL12 stimulation where it co-localizes with CXCL4 (PubMed:14602072). Localization to early endosomes is increased upon CXCL12 stimulation where it co-localizes with DTX3L and CXCL4 (PubMed:24790097). {ECO:0000269|PubMed:14602072, ECO:0000269|PubMed:18819914, ECO:0000269|PubMed:24790097}.
Mouse PG classificationLPG
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