Gene Information
Gene NameTOPBP1
OrganismHomo sapiens (Human)
Gene Length1522
Protein NamesDNA topoisomerase 2-binding protein 1 (DNA topoisomerase II-beta-binding protein 1) (TopBP1) (DNA topoisomerase II-binding protein 1)
Target NameNA
Target TypeNA
Gene Age645 ( ENSG00000163781 )
Evolutionary StageEukaryota
AlphaFoldDBQ92547
Gene CardTOPBP1
Uniprot IDQ92547
PfamPF00533
In ASDno
Allosteric Predictionno (-0.203087095)
Ortholog in AnimalsAlpaca_ TOPBP1 ( ortholog_one2one )
Dog_ TOPBP1 ( ortholog_one2one )
GuineaPig_ TOPBP1 ( ortholog_one2one )
Macaque_ TOPBP1 ( ortholog_one2one )
Mouse_ Topbp1 ( ortholog_one2one )
Pig_ TOPBP1 ( ortholog_one2one )
Rat_ Topbp1 ( ortholog_one2one )
Rabbit_ TOPBP1 ( ortholog_one2one )
OhnologsNA
ParalogsSLF1
TissueNA
Tissue SpecificityHighly expressed in heart, brain, placenta, lung and kidney. {ECO:0000269|PubMed:9461304}.
Pharmacological Animal ModelsNULL(Chimpanzee);NULL(Mouse);NULL(Rat);0.044444(Rabbit)
Gene Ontology
(biological process)
Gene Ontology
(cellular component)
Gene Ontology
(molecular function)
PDB 1WF6  (NMR  2XNH  (X-ray  2.80A  2XNK  (X-ray  2.60A  3AL2  (X-ray  2.00A  3AL3  (X-ray  2.15A  3JVE  (X-ray  1.34A  3OLC  (X-ray  2.40A  3PD7  (X-ray  1.26A  3UEN  (X-ray  1.90A  3UEO  (X-ray  2.60A  6RML  (X-ray  2.81A  6RMM  (X-ray  3.53A  7CMZ  (X-ray  1.70A 
DBSNP rs17301766  rs10935070  rs10935070 
Subcellular location [CC]Nucleus. Cytoplasm, cytoskeleton, microtubule organizing center, centrosome. Cytoplasm, cytoskeleton, spindle pole. Chromosome. Note=Detected on unpaired autosomes in meiotic prophase cells. Detected on X and Y chromosomes during later stages of prophase. Colocalizes with ATR and H2AX at unsynapsed chromosome cores during prophase (By similarity). Has a uniform nuclear distribution during G phase. Colocalizes with BRCA1 at stalled replication forks during S phase. In mitotic cells it colocalizes with BRCA1 at spindle poles and centrosomes during metaphase and anaphase. Detected in discrete foci together with PML and numerous DNA repair enzymes after DNA damage by alkylating agents, UV or gamma irradiation. Localizes to sites of DNA damage in a H2AX- independent manner. {ECO:0000250}.
Mouse PG classificationNA
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