Gene Information
Gene NamePUS1
OrganismHomo sapiens (Human)
Gene Length427
Protein NamesPseudouridylate synthase 1 homolog (EC 5.4.99.-) (tRNA pseudouridine synthase 1) (EC 5.4.99.12) (tRNA pseudouridine(38-40) synthase) (tRNA pseudouridylate synthase I) (tRNA-uridine isomerase I)
Target NameNA
Target TypeNA
Gene Age>4290 ( ENSG00000177192 )
Evolutionary StageEukaryota
AlphaFoldDBQ9Y606
Gene CardPUS1
Uniprot IDQ9Y606
PfamPF01416
In ASDno
Allosteric Predictionno (-1.753093667)
Ortholog in AnimalsAlpaca_ PUS1 ( ortholog_one2one )
Dog_ PUS1 ( ortholog_one2one )
GuineaPig_ PUS1 ( ortholog_one2one )
Macaque_ PUS1 ( ortholog_one2one )
Mouse_ Pus1 ( ortholog_one2one )
Pig_ PUS1 ( ortholog_one2one )
Rat_ Pus1 ( ortholog_one2one )
OhnologsNA
ParalogsPUS3, PUSL1
TissueNA
Tissue SpecificityWidely expressed (PubMed:15108122). High levels of expression found in brain and skeletal muscle (PubMed:15108122). {ECO:0000269|PubMed:15108122}.
Pharmacological Animal ModelsNA
Gene Ontology
(biological process)
Gene Ontology
(cellular component)
Gene Ontology
(molecular function)
PDB 4IQM  (X-ray  1.80A  4ITS  (X-ray  1.85A  4J37  (X-ray  1.75A  4NZ6  (X-ray  2.00A  4NZ7  (X-ray  2.70A 
DBSNP rs76655496  rs104894371 
Subcellular location [CC][Isoform 1]: Mitochondrion {ECO:0000269|PubMed:17056637, ECO:0000305|PubMed:15772074}.;
[Isoform 2]: Nucleus {ECO:0000269|PubMed:17056637, ECO:0000305|PubMed:15772074}. Cytoplasm {ECO:0000305|PubMed:15772074}.
Mouse PG classificationLPG
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