Gene Information
Gene NamePDX1
OrganismHomo sapiens (Human)
Gene Length501
Protein NamesPyruvate dehydrogenase protein X component, mitochondrial (Dihydrolipoamide dehydrogenase-binding protein of pyruvate dehydrogenase complex) (E3-binding protein) (E3BP) (Lipoyl-containing pyruvate dehydrogenase complex component X) (proX)
Target NameNA
Target TypeNA
Gene Age382 ( ENSG00000139515 )
Evolutionary StageEumetazoa
AlphaFoldDBO00330
Gene CardPDHX
Uniprot IDO00330
PfamPF00198; PF00364; PF02817
In ASDno
Allosteric Predictionyes (0.335959373)
Ortholog in AnimalsAlpaca_ PDX1 ( ortholog_one2one )
Dog_ PDX1 ( ortholog_one2one )
GuineaPig_ PDX1 ( ortholog_one2one )
Macaque_ PDX1 ( ortholog_one2one )
Mouse_ Pdx1 ( ortholog_one2one )
Pig_ PDX1 ( ortholog_one2one )
Rat_ Pdx1 ( ortholog_one2one )
Rabbit_ PDX1 ( ortholog_one2one )
OhnologsNA
ParalogsHOXA1, HOXD10, HOXC4, HOXD4, HOXA4, HOXD11, HOXC10, HOXA6, TLX3, HOXA10, HOXB3, HOXD13, HOXD9, HOXB4, HOXD1, HOXB7, HOXD8, HOXC5, HOXD3, HOXA13, HOXB8, HOXC9, HOXA3, HOXA5, HOXC11, HOXB2, HOXD12, GSX2, HOXB5, HOXB9, HOXB1, TLX1, TLX2, HOXA2, HOXA11, HOXC6, HOXA7, HOXB13, HOXC8, HOXC12, HOXC13, HOXB6
Tissueduodenum, pancreas, small.intestine
Tissue SpecificityNA
Pharmacological Animal ModelsNULL(Chimpanzee);NULL(Mouse);0.053256(Rat);0.197862(Rabbit)
Gene Ontology
(biological process)
Gene Ontology
(cellular component)
Gene Ontology
(molecular function)
PDB 1ZY8  (X-ray  2.59A  2DNC  (NMR  2F5Z  (X-ray  2.18A  2F60  (X-ray  1.55A  6H60  (EM  6.00A 
DBSNP rs1049306  rs11539202  rs17850649 
Subcellular location [CC]Mitochondrion matrix.
Mouse PG classificationHPG
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