Gene Information
Gene NameMYOT
OrganismHomo sapiens (Human)
Gene Length498
Protein NamesMyotilin (57 kDa cytoskeletal protein) (Myofibrillar titin-like Ig domains protein) (Titin immunoglobulin domain protein)
Target NameNA
Target TypeNA
Gene Age454 ( ENSG00000120729 )
Evolutionary StageEumetazoa
AlphaFoldDBQ9UBF9
Gene CardMYOT
Uniprot IDQ9UBF9
PfamPF07679
In ASDno
Allosteric Predictionno (-0.674759527)
Ortholog in AnimalsAlpaca_ MYOT ( ortholog_one2one )
Dog_ MYOT ( ortholog_one2one )
GuineaPig_ MYOT ( ortholog_one2one )
Mouse_ Myot ( ortholog_one2one )
Pig_ MYOT ( ortholog_one2one )
Rat_ Myot ( ortholog_one2one )
Rabbit_ MYOT ( ortholog_one2one )
OhnologsNA
ParalogsOBSCN, PALLD, MYPN, HMCN1, IGFN1, CCDC141, ALPK3, SPEG, SPEGNB
Tissueskeletal.muscle, artery, tongue
Tissue SpecificityExpressed in skeletal muscle (at protein level). Expressed in skeletal muscle, heart, bone marrow and thyroid gland. {ECO:0000269|PubMed:10369880, ECO:0000269|PubMed:10486214}.
Pharmacological Animal ModelsNA
Gene Ontology
(biological process)
Gene Ontology
(cellular component)
Gene Ontology
(molecular function)
PDB 2KDG  (NMR  2KKQ  (NMR 
DBSNP rs34717730  rs28937597  rs6890689 
Subcellular location [CC]Cell membrane, sarcolemma {ECO:0000269|PubMed:10369880}. Cytoplasm, cytoskeleton {ECO:0000269|PubMed:10369880}. Cytoplasm, myofibril, sarcomere, Z line {ECO:0000269|PubMed:16076904}. Note=Sarcomeric, also localized to the sarcolemma (PubMed:10369880). Colocalizes with MYOZ1 at the Z-lines in skeletal muscle (PubMed:16076904). {ECO:0000269|PubMed:10369880, ECO:0000269|PubMed:16076904}.
Mouse PG classificationNA
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