Gene Information
Gene NameDMGDH
OrganismHomo sapiens (Human)
Gene Length866
Protein NamesDimethylglycine dehydrogenase, mitochondrial (EC 1.5.8.4) (ME2GLYDH)
Target NameNA
Target TypeNA
Gene Age950 ( ENSG00000132837 )
Evolutionary StageEuk+Bac
AlphaFoldDBQ9UI17
Gene CardDMGDH
Uniprot IDQ9UI17
PfamPF01266; PF16350; PF01571; PF08669
In ASDno
Allosteric Predictionno (-0.155260999)
Ortholog in AnimalsAlpaca_ DMGDH ( ortholog_one2one )
Dog_ DMGDH ( ortholog_one2one )
GuineaPig_ DMGDH ( ortholog_one2one )
Macaque_ DMGDH ( ortholog_one2one )
Mouse_ Dmgdh ( ortholog_one2one )
Pig_ DMGDH ( ortholog_one2one )
Rat_ Dmgdh ( ortholog_one2one )
Rabbit_ DMGDH ( ortholog_one2one )
OhnologsNA
ParalogsYPEL3, YPEL2, AMT, YPEL4, L2HGDH, PDPR, SARDH, FOXRED1, YPEL1, YPEL5
Tissuekidney, liver
Tissue SpecificityNA
Pharmacological Animal Models0.350380(Chimpanzee);0.001000(Mouse);NULL(Rat);NULL(Rabbit)
Gene Ontology
(biological process)
Gene Ontology
(cellular component)
Gene Ontology
(molecular function)
PDB 5L46  (X-ray  3.09A 
DBSNP rs121908331  rs532964  rs1805073  rs1805074 
Subcellular location [CC]Mitochondrion.
Mouse PG classificationNA
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