Gene Information
Gene NameD2HGDH
OrganismHomo sapiens (Human)
Gene Length521
Protein NamesD-2-hydroxyglutarate dehydrogenase, mitochondrial (EC 1.1.99.39)
Target NameNA
Target TypeNA
Gene Age1714 ( ENSG00000180902 )
Evolutionary StageEuk+Bac
AlphaFoldDBQ8N465
Gene CardD2HGDH
Uniprot IDQ8N465
PfamPF02913; PF01565
In ASDno
Allosteric Predictionno (-0.723829708)
Ortholog in AnimalsAlpaca_ D2HGDH ( ortholog_one2one )
Dog_ D2HGDH ( ortholog_one2one )
GuineaPig_ D2HGDH ( ortholog_one2one )
Macaque_ D2HGDH ( ortholog_one2one )
Mouse_ D2hgdh ( ortholog_one2one )
Pig_ D2HGDH ( ortholog_one2one )
Rat_ D2hgdh ( ortholog_one2one )
Rabbit_ D2HGDH ( ortholog_one2one )
OhnologsNA
ParalogsAGPS, LDHD
TissueNA
Tissue SpecificityNA
Pharmacological Animal ModelsNULL(Chimpanzee);NULL(Mouse);NULL(Rat);0.067043(Rabbit)
Gene Ontology
(biological process)
Gene Ontology
(cellular component)
Gene Ontology
(molecular function)
PDB 6LPN  (X-ray  2.21A  6LPP  (X-ray  2.65A  6LPQ  (X-ray  2.80A  6LPT  (X-ray  2.62A  6LPU  (X-ray  2.92A  6LPX  (X-ray  2.80A 
DBSNP rs4675887  rs142050154  rs762857195  rs121434361  rs1432270139  rs773735172  rs587783517  rs750889931  rs374535734  rs1106639  rs1105273  rs267606759  rs746519212  rs199908032  rs146578303  rs121434362  rs121434360  rs746956176  rs1453924640 
Subcellular location [CC]Mitochondrion {ECO:0000305|PubMed:15070399}.
Mouse PG classificationNA
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