Gene Information
Gene NameACE
OrganismHomo sapiens (Human)
Gene Length1306
Protein NamesAngiotensin-converting enzyme (ACE) (EC 3.4.15.1) (Dipeptidyl carboxypeptidase I) (Kininase II) (CD antigen CD143) [Cleaved into: Angiotensin-converting enzyme, soluble form]
Target Nameangiotensin-converting enzyme
Target TypeNA
Gene Age168 ( ENSG00000159640 )
Evolutionary StageEuk+Bac
AlphaFoldDBP12821
Gene CardACE
Uniprot IDP12821
PfamPF01401
In ASDyes
Allosteric Predictionyes (1.383507107)
Ortholog in AnimalsAlpaca_ ACE ( ortholog_one2one )
Dog_ ACE ( ortholog_one2one )
GuineaPig_ ACE ( ortholog_one2one )
Macaque_ ACE ( ortholog_one2one )
Mouse_ Ace ( ortholog_one2one )
Pig_ ACE ( ortholog_one2one )
Rat_ Ace ( ortholog_one2one )
Rabbit_ ACE ( ortholog_one2one )
OhnologsACE2
ParalogsACE2
Tissuesmall.intestine, small.intestine.Peyers.patch
Tissue SpecificityUbiquitously expressed, with highest levels in lung, kidney, heart, gastrointestinal system and prostate. {ECO:0000269|PubMed:10924499, ECO:0000269|PubMed:10969042, ECO:0000269|PubMed:12459472, ECO:0000269|PubMed:15671045}.;
[Isoform Testis-specific]: Specifically expressed in spermatocytes and adult testis. {ECO:0000269|PubMed:2547653, ECO:0000269|PubMed:2554286}.
Pharmacological Animal ModelsNULL(Chimpanzee);NULL(Mouse);0.003490(Rat);0.054545(Rabbit)
Gene Ontology
(biological process)
Gene Ontology
(cellular component)
Gene Ontology
(molecular function)
PDB 1O86  (X-ray  2.00A  1O8A  (X-ray  2.00A  1UZE  (X-ray  1.82A  1UZF  (X-ray  2.00A  2C6F  (X-ray  3.01A  2C6N  (X-ray  3.00A  2IUL  (X-ray  2.01A  2IUX  (X-ray  2.80A  2OC2  (X-ray  2.25A  2XY9  (X-ray  1.97A  2XYD  (X-ray  2.15A  2YDM  (X-ray  2.44A  3BKK  (X-ray  2.17A  3BKL  (X-ray  2.18A  3L3N  (X-ray  2.30A  3NXQ  (X-ray  1.99A  4APH  (X-ray  1.99A  4APJ  (X-ray  2.60A  4BXK  (X-ray  2.20A  4BZR  (X-ray  1.84A  4BZS  (X-ray  2.10A  4C2N  (X-ray  2.59A  4C2O  (X-ray  1.80A  4C2P  (X-ray  1.99A  4C2Q  (X-ray  2.40A  4C2R  (X-ray  2.30A  4CA5  (X-ray  1.85A  4CA6  (X-ray  1.91A  4UFA  (X-ray  1.80A  4UFB  (X-ray  1.80A  5AM8  (X-ray  1.90A  5AM9  (X-ray  1.80A  5AMA  (X-ray  1.80A  5AMB  (X-ray  1.55A  5AMC  (X-ray  1.65A  6EN5  (X-ray  1.75A  6EN6  (X-ray  1.80A  6F9R  (X-ray  1.85A  6F9T  (X-ray  1.60A  6F9U  (X-ray  1.90A  6F9V  (X-ray  1.69A  6H5W  (X-ray  1.37A  6H5X  (X-ray  1.80A  6QS1  (X-ray  1.80A  6TT1  (X-ray  1.80A  6TT3  (X-ray  1.70A  6TT4  (X-ray  1.80A  6ZPQ  (X-ray  1.85A  6ZPT  (X-ray  2.80A  6ZPU  (X-ray  2.00A  7Q24  (X-ray  2.00A  7Q25  (X-ray  1.60A  7Q26  (X-ray  1.70A  7Q27  (X-ray  1.50A  7Q28  (X-ray  1.65A  7Q29  (X-ray  1.60A  7Q3Y  (EM  4.34A  7Q49  (EM  3.72A  7Q4C  (EM  4.08A  7Q4D  (EM  3.78A  7Q4E  (EM  3.63A  7Z6Z  (X-ray  1.75A  7Z70  (X-ray  1.85A 
DBSNP rs13306087  rs12720754  rs3730025  rs4302  rs4303  rs4303  rs989500910  rs2229839  rs56394458  rs13306085  rs12720746  rs4314  rs12709426  rs13306091  rs3730043  rs4976  rs4977  rs12709442  rs121912703  rs4980  rs4364  rs4981  rs4317  rs4318 
Subcellular location [CC]Cell membrane {ECO:0000269|PubMed:12386153};
Single-pass type I membrane protein {ECO:0000255}. Cytoplasm {ECO:0000250|UniProtKB:P09470}. Note=Detected in both cell membrane and cytoplasm in neurons. {ECO:0000250|UniProtKB:P09470}.;
[Angiotensin-converting enzyme, soluble form]: Secreted {ECO:0000269|PubMed:10769174, ECO:0000269|PubMed:11274151, ECO:0000269|PubMed:7499427, ECO:0000269|PubMed:8253769}.;
[Isoform Testis-specific]: Cell membrane {ECO:0000269|PubMed:1668266, ECO:0000269|PubMed:8626443};
Single-pass type I membrane protein {ECO:0000255}. Secreted {ECO:0000269|PubMed:1668266}. Note=The testis-specific isoform can be cleaved before the transmembrane region, releasing a soluble form. {ECO:0000269|PubMed:1668266}.
Mouse PG classificationNA
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