Gene Information
Gene NameDUX4
OrganismHomo sapiens (Human)
Gene Length424
Protein NamesDouble homeobox protein 4 (Double homeobox protein 10)
Target NameNA
Target TypeNA
Gene Age55 ( ENSG00000260596 )
3 ( ENSG00000283949 )
Evolutionary StageEumetazoa
AlphaFoldDBQ9UBX2
Gene CardDUX4
Uniprot IDQ9UBX2
PfamPF00046
In ASDno
Allosteric Predictionno (-0.422264704)
Ortholog in AnimalsMouse_ Duxbl1 ( ortholog_one2one )
Rat_ Dux4 ( ortholog_one2one )
OhnologsNA
ParalogsARGFX, PAX7, PAX3, ALX4, PAX2, UNCX, RAX2, PAX8, DMBX1, DPRX, PAX5, ISX, ALX3, RHOXF2B, RHOXF2, GSC2, SEBOX, RAX, DRGX, ARX, RHOXF1, PITX3, PRRX1, SHOX, SHOX2, PRRX2, OTX2, PAX4, EVX1, PAX1, PITX2, PHOX2A, CRX, PHOX2B, EVX2, ALX1, VSX2, MIXL1, DUXA, PAX6, OTP, HESX1, NOBOX, PROP1, PAX9, GSC, ESX1, DUXB, PITX1, OTX1
TissueNA
Tissue SpecificityIsoform 1: Does not seem to be expressed in normal muscle, but is detected in muscle of individuals with FSHD, and also in testis (at protein level) (PubMed:21060811, PubMed:17984056). Isoform 1: Does not seem to be expressed in normal muscle, but in muscle of individuals with FSHD, where it may be toxic to cells (PubMed:21060811, PubMed:17984056). Isoform 2: Detected in skeletal muscle, fibroblasts and testis from healthy individuals (PubMed:21060811). {ECO:0000269|PubMed:17984056, ECO:0000269|PubMed:21060811}.
Pharmacological Animal ModelsNA
Gene Ontology
(biological process)
Gene Ontology
(cellular component)
Gene Ontology
(molecular function)
PDB 5Z2S  (X-ray  1.50A  5Z2T  (X-ray  2.62A  5Z6Z  (X-ray  2.30A  5ZFW  (X-ray  2.10A  5ZFY  (X-ray  2.30A  5ZFZ  (X-ray  1.90A  6A8R  (X-ray  1.60A  6DFY  (X-ray  2.62A  6E8C  (X-ray  2.12A  6U81  (X-ray  2.34A  6U82  (X-ray  3.21A 
DBSNP NA 
Subcellular location [CC][Isoform 1]: Nucleus {ECO:0000255|PROSITE-ProRule:PRU00108, ECO:0000269|PubMed:15709750, ECO:0000269|PubMed:17984056, ECO:0000269|PubMed:21060811, ECO:0000269|PubMed:26951377, ECO:0000269|PubMed:27378237, ECO:0000269|PubMed:28459457, ECO:0000269|PubMed:29618456}. Note=Actively transported through the nuclear pore complex (NPC). {ECO:0000305|PubMed:15709750}.;
[Isoform 2]: Nucleus {ECO:0000269|PubMed:29618456, ECO:0000305|PubMed:15709750}.
Mouse PG classificationNA
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