Gene Information
Gene NameTARDBP
OrganismHomo sapiens (Human)
Gene Length414
Protein NamesTAR DNA-binding protein 43 (TDP-43)
Target Nametar dna binding protein 43
Target TypeClinical trial target
Gene Age>4290 ( ENSG00000120948 )
Evolutionary StageEumetazoa
AlphaFoldDBQ13148
Gene CardTARDBP
Uniprot IDQ13148
PfamPF00076; PF18694
In ASDyes
Allosteric Predictionyes (0.305945943)
Ortholog in AnimalsAlpaca_ TARDBP ( ortholog_one2one )
Alpaca_ TARDBP ( ortholog_one2many )
Dog_ TARDBP ( ortholog_one2one )
GuineaPig_ TARDBP ( ortholog_one2one )
Macaque_ TARDBP ( ortholog_one2one )
Mouse_ Tardbp ( ortholog_one2one )
Pig_ TARDBP ( ortholog_one2one )
Rat_ Tardbp ( ortholog_one2one )
Rabbit_ TARDBP ( ortholog_one2one )
OhnologsNA
ParalogsRBMS2, PABPC1, PABPC3, RBM24, ELAVL4, ELAVL3, RBMS1, ELAVL2, PUF60, RBM34, RBM45, HNRNPR, SYNCRIP, PABPC1L, PABPC5, RBM14, PABPC1L2A, PABPC1L2B, SF3B4, RBM38, ELAVL1, RBMS3, PABPC4, PABPC4L
TissueNA
Tissue SpecificityUbiquitously expressed. In particular, expression is high in pancreas, placenta, lung, genital tract and spleen.
Pharmacological Animal ModelsNULL(Chimpanzee);NULL(Mouse);NULL(Rat);0.005405(Rabbit)
Gene Ontology
(biological process)
Gene Ontology
(cellular component)
Gene Ontology
(molecular function)
PDB 1WF0  (NMR  2CQG  (NMR  2N2C  (NMR  2N3X  (NMR  2N4G  (NMR  2N4H  (NMR  2N4P  (NMR  4BS2  (NMR  4IUF  (X-ray  2.75A  4Y00  (X-ray  3.00A  4Y0F  (X-ray  2.65A  5MDI  (X-ray  2.10A  5MRG  (NMR  5W50  (X-ray  1.40A  5W52  (EM  1.40A  5W7V  (EM  3.80A  5WHN  (X-ray  1.10A  5WHP  (X-ray  1.00A  5WIA  (X-ray  1.00A  5WIQ  (X-ray  1.25A  5WKB  (EM  1.00A  5WKD  (X-ray  1.80A  5X4F  (NMR  6B1G  (NMR  6CF4  (EM  0.75A  6CFH  (EM  1.50A  6N37  (EM  3.80A  6N3A  (EM  3.30A  6N3B  (EM  3.80A  6N3C  (EM  3.30A  6T4B  (X-ray  2.55A  7KWZ  (EM  3.20A  7N9H  (X-ray  2.20A  7PY2  (EM  2.60A 
DBSNP rs80356715  rs80356717  rs80356718  rs80356719  rs121908395  rs80356721  rs80356721  rs80356723  rs80356723  rs4884357  rs80356726  rs80356727  rs80356728  rs80356729  rs80356730  rs80356731  rs80356733  rs80356735  rs80356739  rs80356738  rs367543041  rs80356741  rs80356742  rs80356743 
Subcellular location [CC]Nucleus {ECO:0000269|PubMed:17023659, ECO:0000269|PubMed:17481916, ECO:0000269|PubMed:18957508, ECO:0000269|PubMed:19765185, ECO:0000269|PubMed:25678563, ECO:0000269|PubMed:28663553, ECO:0000269|PubMed:29438978}. Cytoplasm {ECO:0000269|PubMed:18957508, ECO:0000269|PubMed:23398327, ECO:0000269|PubMed:30464263}. Cytoplasm, Stress granule {ECO:0000269|PubMed:19765185, ECO:0000269|PubMed:23398327}. Mitochondrion {ECO:0000269|PubMed:28794432, ECO:0000269|PubMed:33031745}. Note=Continuously travels in and out of the nucleus (PubMed:18957508). Localizes to stress granules in response to oxidative stress (PubMed:19765185). A small subset localizes in mitochondria (PubMed:28794432). {ECO:0000269|PubMed:18957508, ECO:0000269|PubMed:19765185, ECO:0000269|PubMed:28794432}.
Mouse PG classificationLPG
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