Gene Information
Gene NameRPGRIP1
OrganismHomo sapiens (Human)
Gene Length1286
Protein NamesX-linked retinitis pigmentosa GTPase regulator-interacting protein 1 (RPGR-interacting protein 1)
Target NameNA
Target TypeNA
Gene Age424 ( ENSG00000092200 )
Evolutionary StageEumetazoa
AlphaFoldDBQ96KN7
Gene CardRPGRIP1
Uniprot IDQ96KN7
PfamPF00168; PF11618; PF18111
In ASDno
Allosteric Predictionno (-1.290926467)
Ortholog in AnimalsAlpaca_ RPGRIP1 ( ortholog_one2one )
Dog_ RPGRIP1 ( ortholog_one2one )
GuineaPig_ RPGRIP1 ( ortholog_one2one )
Macaque_ RPGRIP1 ( ortholog_one2one )
Mouse_ Rpgrip1 ( ortholog_one2one )
Pig_ RPGRIP1 ( ortholog_one2one )
Rat_ Rpgrip1 ( ortholog_one2one )
Rabbit_ RPGRIP1 ( ortholog_one2one )
OhnologsRPGRIP1L
ParalogsRPGRIP1L
Tissuetestis
Tissue SpecificityStrong expression in retina, with weaker expression in testis. Expressed in other neurons such as amacrine cells. Colocalizes with RGPR in the outer segment of rod photoreceptors and cone outer segments. {ECO:0000269|PubMed:10958647, ECO:0000269|PubMed:10958648, ECO:0000269|PubMed:12140192}.
Pharmacological Animal ModelsNA
Gene Ontology
(biological process)
Gene Ontology
(cellular component)
Gene Ontology
(molecular function)
PDB 4QAM  (X-ray  1.83A 
DBSNP rs1040904  rs6571751  rs1325466987  rs190985984  rs10151259  rs147586703  rs34067949  rs74034910  rs3748360  rs3748360  rs200325360  rs1010290273  rs61751268  rs758652031  rs142796310  rs372647080  rs28937883  rs373515194  rs772480252  rs181758389  rs61751274  rs35810926  rs3748361  rs201521970  rs17103671  rs34725281 
Subcellular location [CC]Cell projection, cilium {ECO:0000269|PubMed:21685204}. Note=Situated between the axonemal microtubules and the plasma membrane (By similarity). In the retinal photoreceptor cell layer, localizes at the connecting cilium, a thin bridge linking the cell body and the light-sensing outer segment (By similarity). Colocalizes with RGPR in the photoreceptor connecting cilium (By similarity). {ECO:0000250|UniProtKB:Q9EPQ2}.
Mouse PG classificationHPG
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