Gene Information
Gene NamePRPF3
OrganismHomo sapiens (Human)
Gene Length683
Protein NamesU4/U6 small nuclear ribonucleoprotein Prp3 (Pre-mRNA-splicing factor 3) (hPrp3) (U4/U6 snRNP 90 kDa protein)
Target NameNA
Target TypeNA
Gene Age680 ( ENSG00000117360 )
Evolutionary StageEukaryota
AlphaFoldDBO43395
Gene CardPRPF3
Uniprot IDO43395
PfamPF06544; PF08572; PF01480
In ASDno
Allosteric Predictionno (-0.909692542)
Ortholog in AnimalsAlpaca_ PRPF3 ( ortholog_one2one )
Dog_ PRPF3 ( ortholog_one2one )
GuineaPig_ PRPF3 ( ortholog_one2one )
Macaque_ PRPF3 ( ortholog_one2one )
Mouse_ Prpf3 ( ortholog_one2one )
Pig_ PRPF3 ( ortholog_one2one )
Rat_ Prpf3 ( ortholog_one2one )
Rabbit_ PRPF3 ( ortholog_one2one )
OhnologsNA
ParalogsNA
TissueNA
Tissue SpecificityHighly expressed in retina, liver, kidney and blood. Detected at lower levels in heart and brain. {ECO:0000269|PubMed:11773002}.
Pharmacological Animal ModelsNULL(Chimpanzee);NULL(Mouse);NULL(Rat);0.140848(Rabbit)
Gene Ontology
(biological process)
Gene Ontology
(cellular component)
Gene Ontology
(molecular function)
PDB 1X4Q  (NMR  3JCR  (EM  7.00A  5O9Z  (EM  4.50A  6AH0  (EM  5.70A  6AHD  (EM  3.80A  6QW6  (EM  2.92A  6QX9  (EM  3.28A 
DBSNP rs12736964  rs121434242  rs121434241 
Subcellular location [CC]Nucleus {ECO:0000269|PubMed:17932117, ECO:0000269|PubMed:26912367, ECO:0000269|PubMed:28781166, ECO:0000269|PubMed:9328476, ECO:0000269|PubMed:9404889}. Nucleus speckle.
Mouse PG classificationHPG
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