Gene Information
Gene NameSPTBN1
OrganismHomo sapiens (Human)
Gene Length2364
Protein NamesSpectrin beta chain, non-erythrocytic 1 (Beta-II spectrin) (Fodrin beta chain) (Spectrin, non-erythroid beta chain 1)
Target Namespectrin non-erythroid beta chain 1
Target TypeClinical trial target
Gene Age987 ( ENSG00000115306 )
Evolutionary StageEukaryota
AlphaFoldDBQ01082
Gene CardSPTBN1
Uniprot IDQ01082
PfamPF00307; PF15410; PF00435
In ASDno
Allosteric Predictionyes (1.023291773)
Ortholog in AnimalsAlpaca_ SPTBN1 ( ortholog_one2one )
Dog_ SPTBN1 ( ortholog_one2one )
GuineaPig_ SPTBN1 ( ortholog_one2one )
Macaque_ SPTBN1 ( ortholog_one2one )
Mouse_ Sptbn1 ( ortholog_one2one )
Pig_ SPTBN1 ( ortholog_one2one )
Rat_ Sptbn1 ( ortholog_one2one )
OhnologsSPTB, SPTBN2
ParalogsDSP, SPTBN5, ACTN4, MICAL2, DMD, SYNE3, GAS2L2, SPTBN2, FLNB, SPTAN1, SYNE2, PLEC, EPPK1, SYNE1, CLMN, DYTN, MICAL3, PKHD1, SMTNL2, DRP2, UTRN, PKHD1L1, ACTN2, ACTN3, MICAL1, MACF1, ACTN1, DST, SPTB, GAS2L3, FLNC, FLNA, DTNA, SPTA1, DTNB, SPTBN4
TissueNA
Tissue SpecificityIsoform 2 is present in brain, lung and kidney (at protein level). {ECO:0000269|PubMed:11665863}.
Pharmacological Animal ModelsNULL(Chimpanzee);NULL(Mouse);0.001000(Rat);NULL(Rabbit)
Gene Ontology
(biological process)
Gene Ontology
(cellular component)
Gene Ontology
(molecular function)
PDB 1AA2  (X-ray  2.00A  1BKR  (X-ray  1.10A  3EDV  (X-ray  1.95A 
DBSNP rs1572690133  rs1029360897  rs1052790 
Subcellular location [CC]Cytoplasm, cytoskeleton {ECO:0000250|UniProtKB:Q62261}. Cytoplasm, myofibril, sarcomere, M line {ECO:0000250|UniProtKB:Q62261}. Cytoplasm, cytosol {ECO:0000269|PubMed:34211179}. Cell membrane {ECO:0000269|PubMed:34211179}. Note=Colocalizes with ANK2 in a distinct intracellular compartment of neonatal cardiomyocytes. {ECO:0000250|UniProtKB:Q62261}.;
[Isoform 2]: Cell membrane {ECO:0000250};
Peripheral membrane protein {ECO:0000250};
Cytoplasmic side {ECO:0000250}.
Mouse PG classificationNA
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